Heart and Blood Conditions

Double Outlet Right Ventricle

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    • For appointments in Seattle, Bellevue, Everett, Federal Way, Olympia, Tri-Cities and Wenatchee, call 206-987-2515.
    • For appointments in Tacoma and Silverdale, call 253-272-1812.
    • For appointments in Alaska, call 907-339-1945.

    If this is a medical emergency, call 911.

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  • Locations +

    • Seattle Children's Main Campus: 206-987-2515
    • Bellevue Clinic and Surgery Center: 425-454-4644
    • Everett: 425-304-6080
    • South Clinic in Federal Way: 253-838-5878
    • Olympia: 360-459-5009
    • South Sound Cardiology Clinics: 253-272-1812
    • Tri-Cities (Richland): 509-946-0976
    • Wenatchee: 509-662-9266
    • Pediatric Cardiology of Alaska: 907-339-1945
    • Seattle Children's doctors provide many cardiac services at regional sites throughout the Pacific Northwest. See our complete list of Heart Center locations.

  • Refer a patient +

    • If you are a provider, fax a New Appointment Request Form (NARF) (PDF) (DOC) to 206-985-3121 or 866-985-3121 (toll-free).
    • No pre-referral work-up is required for most conditions. If you have already done testing such as an EKG, Holter monitor or echocardiogram, please fax this information as well as relevant clinic notes and the NARF to 206-985-3121 or 866-985-3121 (toll-free).
    • Your patient will be seen as quickly as possible by the provider who is the best match for managing the current problem.
    • View our complete Heart Center Referral Information (PDF).

What is double outlet right ventricle?

Double outlet right ventricle is a rare birth defect of the heart.

The heart has two upper collecting chambers (right and left atrium), two lower pumping chambers (right and left ventricle), one artery leaving the right ventricle (pulmonary artery) and one leaving the left ventricle (aorta). In a normal heart, the aorta leaves the left ventricle, carrying oxygen-rich (red) blood to the body. The pulmonary artery leaves the right ventricle, carrying oxygen-poor (blue) blood to the lungs.

In double outlet right ventricle, both of the heart's "outlets" - the pulmonary artery and the aorta - exit abnormally from the right ventricle. This causes the oxygen-rich and oxygen-poor blood to mix together before leaving the heart.

Many kinds of heart defects fall into the category of double outlet right ventricle. They all share the feature that the aorta and pulmonary artery both exit from the right ventricle. In addition, other parts of the heart may be different.

In double outlet right ventricle, there is almost always a hole in the septum, or wall, between the right and left ventricles, called a ventricular septal defect, that allows blood to mix within the heart. Some children also have a hole in the septum between the right and left atria called an atrial septal defect. They can have other defects too, such as abnormal heart valves (pulmonary stenosis, aortic stenosis or mitral valve abnormalities) or abnormal arteries (coarctation of the aorta or pulmonary atresia).

Double Outlet Right Ventricle in Children

This is a congenital defect. Doctors do not know why it happens. They think it occurs very early in the pregnancy, when the baby's heart is forming, before a woman may even know she is pregnant.

Double outlet right ventricle is rare. About one in every 10,000 babies has this condition.

Double Outlet Right Ventricle at Seattle Children's

Our heart team has treated many children with double outlet right ventricle. We have extensive experience with the surgery these patients require. We also have a pediatric cardiac anesthesia team and a cardiac intensive care unit ready to care for children who undergo heart surgery.

When you come to Seattle Children's, a team of people will take care of your child. Along with your child's cardiologist, you are connected with surgeons, cardiac intensive care unit doctors, cardiac anesthesiologists, neonatologists, nurses, cardiac sonographers, dietitians, child life specialists, social workers and others, if their expertise is needed. We work together to meet all of your child's health needs and help your family through this experience.

Seattle Children's has been treating children since 1907. Our team members are trained in their fields and also in meeting the unique needs of children. For example, the doctors who give your child anesthesia are board certified in pediatric anesthesiology. This means they have extra years of training in how to take care of kids. Our child life specialists know how to help children understand their illnesses and treatments in ways that make sense for their age.

The Adult Congenital Heart Disease Program shared by Seattle Children's and the University of Washington can help with care throughout your child's life.

Contact Us

Contact the Heart Center at 206-987-2015 for a cardiac referral, a second opinion or more information.