Publications

  • Phenylketonuria Scientific Review Conference: State of the Science and Future Research Needs
    Molecular Genetics and Metabolism , 2014 June : 112(2)87-122
  • Assent in Research: the Voices of Adolescents
    J Adolescent Medicine , 2014 May : 54(5)515-20
  • Accepting Brain Death
    N Engl J Med , 2014 Mar. 6 : 370891-94
  • Tracheostomies and Assisted Ventilation in Children with Profound Disabilities: Navigating Family and Professional Values
    Pediatrics , 2014 Feb. : 133(Supplement)S44-S49
  • Parental permission for pilot newborn screening research: guidelines from the NBSTRN
    Pediatrics , 2014 Feb. : 133(2)e410-7
  • Our Children Are Not a Diagnosis: The Experience of Parents Who Continue Their Pregnancy After a Prenatal Diagnosis of Trisomy 13 or 18
    Am J Med Genet A , 2014 Feb. : 164(2)308-18
  • Okumura MJ, Ong T, Dawson D, Nielson D, Lewis N, Richards M, Brindis CD, Kleinhenz ME
    Improving transition from paediatric to adult cystic fibrosis care: programme implementation and evaluation.
    BMJ quality & safety , 2014 Jan. 10
  • Stanojevic S, Stocks J, Bountziouka V, Aurora P, Kirkby J, Bourke S, Carr SB, Gunn E, Prasad A, Rosenfeld M, Bilton D
    The impact of switching to the new global lung function initiative equations on spirometry results in the UK CF Registry.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2013 Dec. 12
  • Elliott M, Heltshe SL, Stamey DC, Cochrane ES, Redding GJ, Debley JS
    Exhaled nitric oxide predicts persistence of wheezing, exacerbations, and decline in lung function in wheezy infants and toddlers.
    Clinical and experimental allergy : journal of the British Society for Allergy and Clinical Immunology , 2013 Dec. : 43(12)1351-61
  • Emerson J, Cochrane E, McNamara S, Kuypers J, Gibson RL, Campbell AP
    Home Self-Collection of Nasal Swabs for Diagnosis of Acute Respiratory Virus Infections in Children With Cystic Fibrosis.
    Journal of the Pediatric Infectious Diseases Society , 2013 Dec. : 2(4)345-351
  • Rosenfeld M, Farrell PM, Kloster M, Swanson JO, Vu T, Brumback L, Acton JD, Castile RG, Colin AA, Conrad CK, Hart MA, Kerby GS, Hiatt PW, Mogayzel PJ, Johnson RC, Davis SD
    Association of lung function, chest radiographs and clinical features in infants with cystic fibrosis.
    The European respiratory journal , 2013 Dec. : 42(6)1545-52
  • Leigh MW, Hazucha MJ, Chawla KK, Baker BR, Shapiro AJ, Brown DE, Lavange LM, Horton BJ, Qaqish B, Carson JL, Davis SD, Dell SD, Ferkol TW, Atkinson JJ, Olivier KN, Sagel SD, Rosenfeld M, Milla C, Lee HS, Krischer J, Zariwala MA, Knowles MR
    Standardizing nasal nitric oxide measurement as a test for primary ciliary dyskinesia.
    Annals of the American Thoracic Society , 2013 Dec. : 10(6)574-81
  • Quality Improvement Ethics: Lessons From the SUPPORT Study
    Am J Bioeth , 2013 Dec. : 13(12)14-19
  • Hoffman LR, Pope CE, Hayden HS, Heltshe S, Levy R, McNamara S, Jacobs MA, Rohmer L, Radey M, Ramsey BW, Brittnacher MJ, Borenstein E, Miller SI
    Escherichia coli Dysbiosis Correlates With Gastrointestinal Dysfunction in Children With Cystic Fibrosis.
    Clinical infectious diseases : an official publication of the Infectious Diseases Society of America , 2013 Nov. 20
  • Lee A, Chen ML, Abeshaus S, Poliakov A, Ojemann JG
    Posterior fossa tumors and their impact on sleep and ventilatory control: a clinical perspective.
    Respiratory physiology & neurobiology , 2013 Nov. 1 : 189(2)261-71
  • McCaughey G, Gilpin DF, Schneiders T, Hoffman LR, McKevitt M, Elborn JS, Tunney MM
    Fosfomycin and tobramycin in combination downregulate nitrate reductase genes narG and narH, resulting in increased activity against Pseudomonas aeruginosa under anaerobic conditions.
    Antimicrobial agents and chemotherapy , 2013 Nov. : 57(11)5406-14
  • Ong T, Ramsey BW
    Modifying disease in cystic fibrosis: current and future therapies on the horizon.
    Current opinion in pulmonary medicine , 2013 Nov. : 19(6)645-51
  • Bakker EM, Borsboom GJ, van der Wiel-Kooij EC, Caudri D, Rosenfeld M, Tiddens HA
    Small airway involvement in cystic fibrosis lung disease: routine spirometry as an early and sensitive marker.
    Pediatric pulmonology , 2013 Nov. : 48(11)1081-8
  • Oxygen and Estrogen
    Hastings Center Report , 2013 Nov. : 43(6)
  • Austin-Tse C, Halbritter J, Zariwala MA, Gilberti RM, Gee HY, Hellman N, Pathak N, Liu Y, Panizzi JR, Patel-King RS, Tritschler D, Bower R, O'Toole E, Porath JD, Hurd TW, Chaki M, Diaz KA, Kohl S, Lovric S, Hwang DY, Braun DA, Schueler M, Airik R, Otto EA, Leigh MW, Noone PG, Carson JL, Davis SD, Pittman JE, Ferkol TW, Atkinson JJ, Olivier KN, Sagel SD, Dell SD, Rosenfeld M, Milla CE, Loges NT, Omran H, Porter ME, King SM, Knowles MR, Drummond IA, Hildebrandt F
    Zebrafish Ciliopathy Screen Plus Human Mutational Analysis Identifies C21orf59 and CCDC65 Defects as Causing Primary Ciliary Dyskinesia.
    American journal of human genetics , 2013 Oct. 3 : 93(4)672-86
  • Iwanaga K, Elliott MS, Vedal S, Debley JS
    Urban particulate matter induces pro-remodeling factors by airway epithelial cells from healthy and asthmatic children.
    Inhalation toxicology , 2013 Oct. : 25(12)653-60
  • Mayer-Hamblett N, Rosenfeld M, Treggiari MM, Konstan MW, Retsch-Bogart G, Morgan W, Wagener J, Gibson RL, Khan U, Emerson J, Thompson V, Elkin EP, Ramsey BW, EPIC, ESCF Investigators
    Standard care versus protocol based therapy for new onset Pseudomonas aeruginosa in cystic fibrosis.
    Pediatric pulmonology , 2013 Oct. : 48(10)943-53
  • Mayer-Hamblett N, Rosenfeld M, Treggiari MM, Konstan MW, Retsch-Bogart G, Morgan W, Wagener J, Gibson RL, Khan U, Emerson J, Thompson V, Elkin EP, Ramsey BW, EPIC, ESCF Investigators
    Standard care versus protocol based therapy for new onset Pseudomonas aeruginosa in cystic fibrosis.
    Pediatric pulmonology , 2013 Oct. : 48(10)943-53
  • Mayer-Hamblett N, Rosenfeld M, Treggiari MM, Konstan MW, Retsch-Bogart G, Morgan W, Wagener J, Gibson RL, Khan U, Emerson J, Thompson V, Elkin EP, Ramsey BW, EPIC, ESCF Investigators
    Standard care versus protocol based therapy for new onset Pseudomonas aeruginosa in cystic fibrosis.
    Pediatric pulmonology , 2013 Oct. : 48(10)943-53
  • Ren CL, Konstan MW, Rosenfeld M, Pasta DJ, Millar SJ, Morgan WJ, for the Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis
    Early childhood wheezing is associated with lower lung function in cystic fibrosis.
    Pediatric pulmonology , 2013 Oct. 1
  • Morgan WJ, Wagener JS, Yegin A, Pasta DJ, Millar SJ, Konstan MW, Scientific Advisory Group, investigators, coordinators of the Epidemiologic Study of Cystic Fibrosis
    Probability of treatment following acute decline in lung function in children with cystic fibrosis is related to baseline pulmonary function.
    The Journal of pediatrics , 2013 Oct. : 163(4)1152-7.e2
  • Challenging Cases in Research Ethics
    Am J Bioeth , 2013 Oct. : 13(10)60
  • The ethics of contacting family members of a subject in a genetic research study to return results for an autosomal dominant syndrome
    Am J Bioeth , 2013 Oct. : 13(10)61
  • Managing disclosure of research misconduct by a graduate student to a university mental health professional during a clinical counseling session
    Am J Bioeth , 2013 Oct. : 13(10)68
  • Soares JJ, Deutsch GH, Moore PE, Fazili MF, Austin ED, Brown RF, Sokolow AG, Hilmes MA, Young LR
    Childhood interstitial lung diseases: an 18-year retrospective analysis.
    Pediatrics , 2013 Oct. : 132(4)684-91
  • Psoter KJ, Rosenfeld M
    Opportunities and pitfalls of registry data for clinical research.
    Paediatric respiratory reviews , 2013 Sept. : 14(3)141-5
  • Loeve M, Krestin GP, Rosenfeld M, de Bruijne M, Stick SM, Tiddens HA
    Chest computed tomography: a validated surrogate endpoint of cystic fibrosis lung disease?
    The European respiratory journal , 2013 Sept. : 42(3)844-57
  • Mayer-Hamblett N, Saiman L, Lands LC, Anstead M, Rosenfeld M, Kloster M, Fisher L, Ratjen F
    Impact of acute antibiotic therapy on the pulmonary exacerbation endpoint in cystic fibrosis clinical trials.
    Contemporary clinical trials , 2013 Sept. : 36(1)99-105
  • Subbarao P, Stanojevic S, Brown M, Jensen R, Rosenfeld M, Davis S, Brumback L, Gustafsson P, Ratjen F
    Lung clearance index as an outcome measure for clinical trials in young children with cystic fibrosis. A pilot study using inhaled hypertonic saline.
    American journal of respiratory and critical care medicine , 2013 Aug. 15 : 188(4)456-60
  • Guo DC, Regalado E, Casteel DE, Santos-Cortez RL, Gong L, Kim JJ, Dyack S, Horne SG, Chang G, Jondeau G, Boileau C, Coselli JS, Li Z, Leal SM, Shendure J, Rieder MJ, Bamshad MJ, Nickerson DA, GenTAC Registry Consortium, National Heart, Lung, and Blood Institute Grand Opportunity Exome Sequencing Project, Kim C, Milewicz DM
    Recurrent gain-of-function mutation in PRKG1 causes thoracic aortic aneurysms and acute aortic dissections.
    American journal of human genetics , 2013 Aug. 8 : 93(2)398-404
  • Hjeij R, Lindstrand A, Francis R, Zariwala MA, Liu X, Li Y, Damerla R, Dougherty GW, Abouhamed M, Olbrich H, Loges NT, Pennekamp P, Davis EE, Carvalho CM, Pehlivan D, Werner C, Raidt J, Köhler G, Häffner K, Reyes-Mugica M, Lupski JR, Leigh MW, Rosenfeld M, Morgan LC, Knowles MR, Lo CW, Katsanis N, Omran H
    ARMC4 mutations cause primary ciliary dyskinesia with randomization of left/right body asymmetry.
    American journal of human genetics , 2013 Aug. 8 : 93(2)357-67
  • Zariwala MA, Gee HY, Kurkowiak M, Al-Mutairi DA, Leigh MW, Hurd TW, Hjeij R, Dell SD, Chaki M, Dougherty GW, Adan M, Spear PC, Esteve-Rudd J, Loges NT, Rosenfeld M, Diaz KA, Olbrich H, Wolf WE, Sheridan E, Batten TF, Halbritter J, Porath JD, Kohl S, Lovric S, Hwang DY, Pittman JE, Burns KA, Ferkol TW, Sagel SD, Olivier KN, Morgan LC, Werner C, Raidt J, Pennekamp P, Sun Z, Zhou W, Airik R, Natarajan S, Allen SJ, Amirav I, Wieczorek D, Landwehr K, Nielsen K, Schwerk N, Sertic J, Köhler G, Washburn J, Levy S, Fan S, Koerner-Rettberg C, Amselem S, Williams DS, Mitchell BJ, Drummond IA, Otto EA, Omran H, Knowles MR, Hildebrandt F
    ZMYND10 is mutated in primary ciliary dyskinesia and interacts with LRRC6.
    American journal of human genetics , 2013 Aug. 8 : 93(2)336-45
  • Khorsand D, Song KM, Swanson J, Alessio A, Redding G, Waldhausen J
    Iatrogenic radiation exposure to patients with early onset spine and chest wall deformities.
    Spine , 2013 Aug. 1 : 38(17)E1108-14
  • Redding GJ, Kuo W, Swanson JO, Phillips GS, Emerson J, Yung D, Swanson JW, Sawin RS, Avansino JR
    Upper thoracic shape in children with pectus excavatum: impact on lung function.
    Pediatric pulmonology , 2013 Aug. : 48(8)817-23
  • Kurland G, Deterding RR, Hagood JS, Young LR, Brody AS, Castile RG, Dell S, Fan LL, Hamvas A, Hilman BC, Langston C, Nogee LM, Redding GJ, American Thoracic Society Committee on Childhood Interstitial Lung Disease (chILD) and the chILD Research Network
    An official American Thoracic Society clinical practice guideline: classification, evaluation, and management of childhood interstitial lung disease in infancy.
    American journal of respiratory and critical care medicine , 2013 Aug. 1 : 188(3)376-94
  • Wolter DJ, Emerson JC, McNamara S, Buccat AM, Qin X, Cochrane E, Houston LS, Rogers GB, Marsh P, Prehar K, Pope CE, Blackledge M, Déziel E, Bruce KD, Ramsey BW, Gibson RL, Burns JL, Hoffman LR
    Staphylococcus aureus small-colony variants are independently associated with worse lung disease in children with cystic fibrosis.
    Clinical infectious diseases : an official publication of the Infectious Diseases Society of America , 2013 Aug. : 57(3)384-91
  • Wolter DJ, Emerson JC, McNamara S, Buccat AM, Qin X, Cochrane E, Houston LS, Rogers GB, Marsh P, Prehar K, Pope CE, Blackledge M, Déziel E, Bruce KD, Ramsey BW, Gibson RL, Burns JL, Hoffman LR
    Staphylococcus aureus small-colony variants are independently associated with worse lung disease in children with cystic fibrosis.
    Clinical infectious diseases : an official publication of the Infectious Diseases Society of America , 2013 Aug. : 57(3)384-91
  • Stick S, Tiddens H, Aurora P, Gustafsson P, Ranganathan S, Robinson P, Rosenfeld M, Sly P, Ratjen F
    Early intervention studies in infants and preschool children with cystic fibrosis: are we ready?
    The European respiratory journal , 2013 Aug. : 42(2)527-38
  • Recommendations for returning genomic incidental findings? We need to talk!
    Genet Med , 2013 Aug. : 15(11)85459
  • Growing Up in the Genomic Era: Implications of Whole-Genome Sequencing for Children, Families and Pediatric Practice
    Annu Rev Genomics Hum Genet , 2013 Aug. : 14535-55
  • Fuzzy Images: Ethical Implications of Using Routine Neuroimaging in Premature Neonates to Predict Neurologic Outcomes
    J Pediatr , 2013 Aug. : 163(2)587-592
  • Byrnes CA, Vidmar S, Cheney JL, Carlin JB, Armstrong DS, Cooper PJ, Grimwood K, Moodie M, Robertson CF, Rosenfeld M, Tiddens HA, Wainwright CE, ACFBAL Study Investigators
    Prospective evaluation of respiratory exacerbations in children with cystic fibrosis from newborn screening to 5 years of age.
    Thorax , 2013 July : 68(7)643-51
  • Byrnes CA, Vidmar S, Cheney JL, Carlin JB, Armstrong DS, Cooper PJ, Grimwood K, Moodie M, Robertson CF, Rosenfeld M, Tiddens HA, Wainwright CE, ACFBAL Study Investigators
    Prospective evaluation of respiratory exacerbations in children with cystic fibrosis from newborn screening to 5 years of age.
    Thorax , 2013 July : 68(7)643-51
  • Mayer-Hamblett N, Rosenfeld M, Treggiari MM, Konstan MW, Retsch-Bogart G, Morgan W, Wagener J, Gibson RL, Khan U, Emerson J, Thompson V, Elkin EP, Ramsey BW, for the EPIC, ESCF Investigators
    Standard care versus protocol based therapy for new onset Pseudomonas aeruginosa in cystic fibrosis.
    Pediatric pulmonology , 2013 July
  • Enhancing Children Against Unhealthy Behaviors An Ethical and Policy Assessment of Using a Nicotine Vaccine
    Public Health Ethics , 2013 July : 6(2)197-206
  • Ghosh PS, Taute CT
    A diabetic child with lesions over his legs. Necrobiosis lipoidica diabeticorum.
    Journal of paediatrics and child health , 2013 July : 49(7)598, 600
  • The OHRP and SUPPORT
    The New England journal of medicine , 2013 June 5
  • Rogers GB, Hoffman LR, Carroll MP, Bruce KD
    Interpreting infective microbiota: the importance of an ecological perspective.
    Trends in microbiology , 2013 June : 21(6)271-6
  • Hoffman L, Surette M
    What to expect when you're expectorating: cystic fibrosis exacerbations and microbiota.
    Annals of the American Thoracic Society , 2013 June : 10(3)249-50
  • Subbarao P, Stanojevic S, Brown M, Jensen R, Rosenfeld M, Davis S, Brumback L, Gustafsson P, Ratjen F
    Lung Clearance Index as an Outcome Measure for Clinical Trials in Young Children with Cystic Fibrosis: A Pilot Study using Inhaled Hypertonic Saline.
    American journal of respiratory and critical care medicine , 2013 June
  • Peterson-Carmichael SL, Rosenfeld M, Ascher SB, Hornik CP, Arets HG, Davis SD, Hall GL
    Survey of clinical infant lung function testing practices.
    Pediatric pulmonology , 2013 June
  • Mayer-Hamblett N, Saiman L, Lands LC, Anstead M, Rosenfeld M, Kloster M, Fisher L, Ratjen F
    Impact of acute antibiotic therapy on the pulmonary exacerbation endpoint in cystic fibrosis clinical trials.
    Contemporary clinical trials , 2013 June : 36(1)99-105
  • Examining Palliative Care Team Involvement in Automatic Consultations for Children on Extracorporeal Life Support in the Pediatric Intensive Care Unit
    J Palliat Med , 2013 May 13 : 16(5)492-95
  • Psoter KJ, Rosenfeld M
    Opportunities and pitfalls of registry data for clinical research.
    Paediatric respiratory reviews , 2013 May
  • Rosenfeld M, Farrell PM, Kloster M, Swanson JO, Vu T, Brumback L, Acton JD, Castile RG, Colin AA, Conrad CK, Hart MA, Kerby GS, Hiatt PW, Mogayzel PJ, Johnson RC, Davis SD
    Association of lung function, Chest radiographs and clinical features in infants with cystic fibrosis.
    The European respiratory journal , 2013 May
  • Norton N, Li D, Rampersaud E, Morales A, Martin ER, Zuchner S, Guo S, Gonzalez M, Hedges DJ, Robertson PD, Krumm N, Nickerson DA, Hershberger RE, National Heart, Lung, and Blood Institute GO Exome Sequencing Project and the Exome Sequencing Project Family Studies Project Team
    Exome sequencing and genome-wide linkage analysis in 17 families illustrate the complex contribution of TTN truncating variants to dilated cardiomyopathy.
    Circulation. Cardiovascular genetics , 2013 Apr, : 6(2)144-53
  • Rogers GB, Cuthbertson L, Hoffman LR, Wing PA, Pope C, Hooftman DA, Lilley AK, Oliver A, Carroll MP, Bruce KD, van der Gast CJ
    Reducing bias in bacterial community analysis of lower respiratory infections.
    The ISME journal , 2013 Apr, : 7(4)697-706
  • Ruddy J, Emerson J, Moss R, Genatossio A, McNamara S, Burns JL, Anderson G, Rosenfeld M
    Sputum tobramycin concentrations in cystic fibrosis patients with repeated administration of inhaled tobramycin.
    Journal of aerosol medicine and pulmonary drug delivery , 2013 Apr, : 26(2)69-75
  • Rosenfeld M, Allen J, Arets BH, Aurora P, Beydon N, Calogero C, Castile RG, Davis SD, Fuchs S, Gappa M, Gustaffson PM, Hall GL, Jones MH, Kirkby JC, Kraemer R, Lombardi E, Lum S, Mayer OH, Merkus P, Nielsen KG, Oliver C, Oostveen E, Ranganathan S, Ren CL, Robinson PD, Seddon PC, Sly PD, Sockrider MM, Sonnappa S, Stocks J, Subbarao P, Tepper RS, Vilozni D, American Thoracic Society Assembly on Pediatrics Working Group on Infant and Preschool Lung Function Testing
    An official American Thoracic Society workshop report: optimal lung function tests for monitoring cystic fibrosis, bronchopulmonary dysplasia, and recurrent wheezing in children less than 6 years of age.
    Annals of the American Thoracic Society , 2013 Apr, : 10(2)S1-S11
  • Ruddy J, Emerson J, Moss R, Genatossio A, McNamara S, Burns JL, Anderson G, Rosenfeld M
    Sputum tobramycin concentrations in cystic fibrosis patients with repeated administration of inhaled tobramycin.
    Journal of aerosol medicine and pulmonary drug delivery , 2013 Apr, : 26(2)69-75
  • Rosenfeld M, Allen J, Arets BH, Aurora P, Beydon N, Calogero C, Castile RG, Davis SD, Fuchs S, Gappa M, Gustaffson PM, Hall GL, Jones MH, Kirkby JC, Kraemer R, Lombardi E, Lum S, Mayer OH, Merkus P, Nielsen KG, Oliver C, Oostveen E, Ranganathan S, Ren CL, Robinson PD, Seddon PC, Sly PD, Sockrider MM, Sonnappa S, Stocks J, Subbarao P, Tepper RS, Vilozni D, American Thoracic Society Assembly on Pediatrics Working Group on Infant and Preschool Lung Function Testing
    An official American Thoracic Society workshop report: optimal lung function tests for monitoring cystic fibrosis, bronchopulmonary dysplasia, and recurrent wheezing in children less than 6 years of age.
    Annals of the American Thoracic Society , 2013 Apr, : 10(2)S1-S11
  • Antony D, Becker-Heck A, Zariwala MA, Schmidts M, Onoufriadis A, Forouhan M, Wilson R, Taylor-Cox T, Dewar A, Jackson C, Goggin P, Loges NT, Olbrich H, Jaspers M, Jorissen M, Leigh MW, Wolf WE, Daniels ML, Noone PG, Ferkol TW, Sagel SD, Rosenfeld M, Rutman A, Dixit A, O'Callaghan C, Lucas JS, Hogg C, Scambler PJ, Emes RD, Uk10k, Chung EM, Shoemark A, Knowles MR, Omran H, Mitchison HM
    Mutations in CCDC39 and CCDC40 are the major cause of primary ciliary dyskinesia with axonemal disorganization and absent inner dynein arms.
    Human mutation , 2013 Mar. : 34(3)462-72
  • Antony D, Becker-Heck A, Zariwala MA, Schmidts M, Onoufriadis A, Forouhan M, Wilson R, Taylor-Cox T, Dewar A, Jackson C, Goggin P, Loges NT, Olbrich H, Jaspers M, Jorissen M, Leigh MW, Wolf WE, Daniels ML, Noone PG, Ferkol TW, Sagel SD, Rosenfeld M, Rutman A, Dixit A, O'Callaghan C, Lucas JS, Hogg C, Scambler PJ, Emes RD, Uk10k, Chung EM, Shoemark A, Knowles MR, Omran H, Mitchison HM
    Mutations in CCDC39 and CCDC40 are the major cause of primary ciliary dyskinesia with axonemal disorganization and absent inner dynein arms.
    Human mutation , 2013 Mar. : 34(3)462-72
  • Stick S, Tiddens H, Aurora P, Gustafsson P, Ranganathan S, Robinson P, Rosenfeld M, Sly P, Ratjen F
    Early intervention studies in infants and preschool children with cystic fibrosis: are we ready?
    The European respiratory journal , 2013 Mar.
  • Singleton RJ, Valery PC, Morris P, Byrnes CA, Grimwood K, Redding G, Torzillo PJ, McCallum G, Chikoyak L, Mobberly C, Holman RC, Chang AB
    Indigenous children from three countries with non-cystic fibrosis chronic suppurative lung disease/bronchiectasis.
    Pediatric pulmonology , 2013 Feb. 8
  • Bakker EM, Borsboom GJ, van der Wiel-Kooij EC, Caudri D, Rosenfeld M, Tiddens HA
    Small airway involvement in cystic fibrosis lung disease: Routine spirometry as an early and sensitive marker.
    Pediatric pulmonology , 2013 Feb.
  • Obstructive Sleep Apnea in a 17-Year-Old With Profound Cognitive Impairment
    Pediatrics , 2013 Feb. : 131(3)581-5
  • Role for CTSAs in Leveraging a Distributed Research Infrastructure to Engage Diverse Stakeholders in Emergent Research Policy Development
    Clin Transl Sci , 2013 Feb. : 6(1)57-9
  • The Establishment of Research Ethics Consultation Services (RECS): An Emerging Research Resource
    Clin Transl Sci , 2013 Feb. : 6(1)40-4
  • Fu W, O'Connor TD, Jun G, Kang HM, Abecasis G, Leal SM, Gabriel S, Rieder MJ, Altshuler D, Shendure J, Nickerson DA, Bamshad MJ, NHLBI Exome Sequencing Project, Akey JM
    Analysis of 6,515 exomes reveals the recent origin of most human protein-coding variants.
    Nature , 2013 Jan. 10 : 493(7431)216-20
  • Knowles MR, Leigh MW, Ostrowski LE, Huang L, Carson JL, Hazucha MJ, Yin W, Berg JS, Davis SD, Dell SD, Ferkol TW, Rosenfeld M, Sagel SD, Milla CE, Olivier KN, Turner EH, Lewis AP, Bamshad MJ, Nickerson DA, Shendure J, Zariwala MA, Genetic Disorders of Mucociliary Clearance Consortium
    Exome sequencing identifies mutations in CCDC114 as a cause of primary ciliary dyskinesia.
    American journal of human genetics , 2013 Jan. 10 : 92(1)99-106
  • American Thoracic Society clinical practice guideline: classification, evaluation, and management of childhood interstitial lung disease in infancy
    Am J Respir Crit Care Med , 2013 : 188(3)376-394
  • The International Study of Asthma and Allergies in Childhood (ISAAC) Phase Three: a global synthesis
    J Aller , 2013 : 41(2)73-85
  • Longitudinal nasopharyngeal carriage and antiobiotic resistance of respiratory bacteria in Indigenous Australian and Alaska Native children with bronchiectasis
    PLoS one , 2013 : 5(8)e70478
  • Obstructive lung disease is common in patients with syndromic and congenital scoliosis: A Preliminary Study
    J Pediatr Ortho , 2013 : 33781-785
  • Miazgowicz MM, Elliott MS, Debley JS, Ziegler SF
    Respiratory syncytial virus induces functional thymic stromal lymphopoietin receptor in airway epithelial cells.
    Journal of inflammation research , 2013 : 653-61
  • O'Connor TD, Kiezun A, Bamshad M, Rich SS, Smith JD, Turner E, NHLBIGO Exome Sequencing Project, ESP Population Genetics, Statistical Analysis Working Group, Leal SM, Akey JM
    Fine-scale patterns of population stratification confound rare variant association tests.
    PloS one , 2013 : 8(7)e65834
  • Hoffman LR, Ramsey BW
    Cystic fibrosis therapeutics: the road ahead.
    Chest , 2013 Jan. : 143(1)207-13
  • A Standardized Process of Cystic Fibrosis Related Diabetes Screening in Adolescents: A Single Centers Experience to Improve Screening and Education
    Pediatr Pulmonol , 2013 : 48(S36)A525
  • Brumback LC, Davis SD, Kerby GS, Kloster M, Johnson R, Castile R, Hiatt PW, Hart M, Rosenfeld M
    Lung function from infancy to preschool in a cohort of children with cystic fibrosis.
    The European respiratory journal , 2013 Jan. : 41(1)60-6
  • Reference equations
    Diagnostic Techniques for the Pediatric Pulmonologist , 2013
  • Brumback LC, Davis SD, Kerby GS, Kloster M, Johnson R, Castile R, Hiatt PW, Hart M, Rosenfeld M
    Lung function from infancy to preschool in a cohort of children with cystic fibrosis.
    The European respiratory journal , 2013 Jan. : 41(1)60-6
  • Knowles MR, Leigh MW, Ostrowski LE, Huang L, Carson JL, Hazucha MJ, Yin W, Berg JS, Davis SD, Dell SD, Ferkol TW, Rosenfeld M, Sagel SD, Milla CE, Olivier KN, Turner EH, Lewis AP, Bamshad MJ, Nickerson DA, Shendure J, Zariwala MA, Genetic Disorders of Mucociliary Clearance Consortium
    Exome sequencing identifies mutations in CCDC114 as a cause of primary ciliary dyskinesia.
    American journal of human genetics , 2013 Jan. : 92(1)99-106
  • Cystic Fibrosis
    Nelson Essentials of Pediatrics, 7th Edition , 2013 : Marcdante K, Kliegman RM, Jenson HB, Behrman RE, editors(Saunders Elsevier, Philadelphia, PA. 2013)
  • Respiratory System Assessment
    Nelson Essentials of Pediatrics, 7th Edition , 2013 : . Marcdante K, Kliegman RM, Jenson HB, Behrman RE, editors(Saunders Elsevier, Philadelphia, PA)
  • Loeve M, Krestin GP, Rosenfeld M, de Bruijne M, Stick SM, Tiddens HA
    Chest computed tomography; a validated surrogate endpoint of cystic fibrosis lung disease?
    The European respiratory journal , 2012 Dec.
  • Lee HC, Headley MB, Loo YM, Berlin A, Gale M Jr, Debley JS, Lukacs NW, Ziegler SF
    Thymic stromal lymphopoietin is induced by respiratory syncytial virus-infected airway epithelial cells and promotes a type 2 response to infection.
    The Journal of allergy and clinical immunology , 2012 Nov. : 130(5)1187-1196.e5
  • Stressmann FA, Rogers GB, van der Gast CJ, Marsh P, Vermeer LS, Carroll MP, Hoffman L, Daniels TW, Patel N, Forbes B, Bruce KD
    Long-term cultivation-independent microbial diversity analysis demonstrates that bacterial communities infecting the adult cystic fibrosis lung show stability and resilience.
    Thorax , 2012 Oct. : 67(10)867-73
  • Li-Fraumeni Syndrome: Report of a Clinical Research Workshop and Creation of a Research Consortium
    Cancer Genet , 2012 Oct. : 205(10)479-87
  • Rosenfeld M, Emerson J, McNamara S, Thompson V, Ramsey BW, Morgan W, Gibson RL, EPIC Study Group
    Risk factors for age at initial Pseudomonas acquisition in the cystic fibrosis epic observational cohort.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2012 Sept. : 11(5)446-53
  • Rosenfeld M, Bernardo-Ocampo C, Emerson J, Genatossio A, Burns J, Gibson R
    Prevalence of cystic fibrosis pathogens in the oropharynx of healthy children and implications for cystic fibrosis care.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2012 Sept. : 11(5)456-7
  • Chang AB, Marsh RL, Smith-Vaughan HC, Hoffman LR
    Emerging drugs for bronchiectasis.
    Expert opinion on emerging drugs , 2012 Sept. : 17(3)361-78
  • Rosenfeld M, Emerson J, McNamara S, Thompson V, Ramsey BW, Morgan W, Gibson RL, EPIC Study Group
    Risk factors for age at initial Pseudomonas acquisition in the cystic fibrosis epic observational cohort.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2012 Sept. : 11(5)446-53
  • Rosenfeld M, Bernardo-Ocampo C, Emerson J, Genatossio A, Burns J, Gibson R
    Prevalence of cystic fibrosis pathogens in the oropharynx of healthy children and implications for cystic fibrosis care.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2012 Sept. : 11(5)456-7
  • Rosenfeld M, Emerson J, McNamara S, Thompson V, Ramsey BW, Morgan W, Gibson RL, EPIC Study Group
    Risk factors for age at initial Pseudomonas acquisition in the cystic fibrosis epic observational cohort.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2012 Sept. : 11(5)446-53
  • Beskow LM, Fullerton SM, Namey EE, Nelson DK, Davis AM, Wilfond BS
    Recommendations for ethical approaches to genotype-driven research recruitment.
    Human genetics , 2012 Sept. : 131(9)1423-31
  • Anstead M, Heltshe SL, Khan U, Barbieri JT, Langkamp M, Döring G, Dharia S, Gibson RL, Treggiari MM, Lymp J, Rosenfeld M, Ramsey B
    Pseudomonas aeruginosa serology and risk for re-isolation in the EPIC trial.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2012 Aug. 31
  • Anstead M, Heltshe SL, Khan U, Barbieri JT, Langkamp M, Döring G, Dharia S, Gibson RL, Treggiari MM, Lymp J, Rosenfeld M, Ramsey B
    Pseudomonas aeruginosa serology and risk for re-isolation in the EPIC trial.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2012 Aug. 31
  • Chen ML, Olson HC, Picciano JF, Starr JR, Owens J
    Sleep problems in children with fetal alcohol spectrum disorders.
    Journal of clinical sleep medicine : JCSM : official publication of the American Academy of Sleep Medicine , 2012 Aug. 15 : 8(4)421-9
  • Debley JS, Cochrane ES, Redding GJ, Carter ER
    Lung function and biomarkers of airway inflammation during and after hospitalization for acute exacerbations of childhood asthma associated with viral respiratory symptoms.
    Annals of allergy, asthma & immunology : official publication of the American College of Allergy, Asthma, & Immunology , 2012 Aug. : 109(2)114-20
  • Debley JS, Cochrane ES, Redding GJ, Carter ER
    Lung function and biomarkers of airway inflammation during and after hospitalization for acute exacerbations of childhood asthma associated with viral respiratory symptoms.
    Annals of allergy, asthma & immunology : official publication of the American College of Allergy, Asthma, & Immunology , 2012 Aug. : 109(2)114-20
  • Anstead M, Heltshe SL, Khan U, Barbieri JT, Langkamp M, Döring G, Dharia S, Gibson RL, Treggiari MM, Lymp J, Rosenfeld M, Ramsey B
    Pseudomonas aeruginosa serology and risk for re-isolation in the EPIC trial.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2012 Aug.
  • Janvier A, Farlow B, Wilfond BS
    The experience of families with children with trisomy 13 and 18 in social networks.
    Pediatrics , 2012 Aug. : 130(2)293-8
  • Emond MJ, Louie T, Emerson J, Zhao W, Mathias RA, Knowles MR, Wright FA, Rieder MJ, Tabor HK, Nickerson DA, Barnes KC, National Heart, Lung, and Blood Institute (NHLBI) GO Exome Sequencing Project, Lung GO, Gibson RL, Bamshad MJ
    Exome sequencing of extreme phenotypes identifies DCTN4 as a modifier of chronic Pseudomonas aeruginosa infection in cystic fibrosis.
    Nature genetics , 2012 July 8 : 44(8)886-9
  • Emond MJ, Louie T, Emerson J, Zhao W, Mathias RA, Knowles MR, Wright FA, Rieder MJ, Tabor HK, Nickerson DA, Barnes KC, National Heart, Lung, and Blood Institute (NHLBI) GO Exome Sequencing Project, Lung GO, Gibson RL, Bamshad MJ
    Exome sequencing of extreme phenotypes identifies DCTN4 as a modifier of chronic Pseudomonas aeruginosa infection in cystic fibrosis.
    Nature genetics , 2012 July : 44(8)886-9
  • Predicting our future: lessons from Winnie-the-Pooh.
    The Hastings Center report , 2012 July : 42(4)3
  • Rosenfeld M, Ratjen F, Brumback L, Daniel S, Rowbotham R, McNamara S, Johnson R, Kronmal R, Davis SD, ISIS Study Group
    Inhaled hypertonic saline in infants and children younger than 6 years with cystic fibrosis: the ISIS randomized controlled trial.
    JAMA : the journal of the American Medical Association , 2012 June 6 : 307(21)2269-77
  • Kerby GS, Rosenfeld M, Ren CL, Mayer OH, Brumback L, Castile R, Hart MA, Hiatt P, Kloster M, Johnson R, Jones P, Davis SD
    Lung function distinguishes preschool children with CF from healthy controls in a multi-center setting.
    Pediatric pulmonology , 2012 June : 47(6)597-605
  • Ren CL, Rosenfeld M, Mayer OH, Davis SD, Kloster M, Castile RG, Hiatt PW, Hart M, Johnson R, Jones P, Brumback LC, Kerby GS
    Analysis of the associations between lung function and clinical features in preschool children with cystic fibrosis.
    Pediatric pulmonology , 2012 June : 47(6)574-81
  • Simon TD, Whitlock KB, Riva-Cambrin J, Kestle JR, Rosenfeld M, Dean JM, Holubkov R, Langley M, Hamblett NM
    Revision surgeries are associated with significant increased risk of subsequent cerebrospinal fluid shunt infection.
    The Pediatric infectious disease journal , 2012 June : 31(6)551-6
  • Simon TD, Whitlock KB, Riva-Cambrin J, Kestle JR, Rosenfeld M, Dean JM, Holubkov R, Langley M, Hamblett NM
    Revision surgeries are associated with significant increased risk of subsequent cerebrospinal fluid shunt infection.
    The Pediatric infectious disease journal , 2012 June : 31(6)551-6
  • Rosenfeld M, Ratjen F, Brumback L, Daniel S, Rowbotham R, McNamara S, Johnson R, Kronmal R, Davis SD, ISIS Study Group
    Inhaled hypertonic saline in infants and children younger than 6 years with cystic fibrosis: the ISIS randomized controlled trial.
    JAMA : the journal of the American Medical Association , 2012 June : 307(21)2269-77
  • Bulkow LR, Singleton RJ, DeByle C, Miernyk K, Redding G, Hummel KB, Chikoyak L, Hennessy TW
    Risk factors for hospitalization with lower respiratory tract infections in children in rural Alaska.
    Pediatrics , 2012 May : 129(5)e1220-7
  • Debley J, Stanojevic S, Filbrun AG, Subbarao P
    Bronchodilator responsiveness in wheezy infants and toddlers is not associated with asthma risk factors.
    Pediatric pulmonology , 2012 May : 47(5)421-8
  • Quon BS, Patrick DL, Edwards TC, Aitken ML, Gibson RL, Genatossio A, McNamara S, Goss CH
    Feasibility of using pedometers to measure daily step counts in cystic fibrosis and an assessment of its responsiveness to changes in health state.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2012 May : 11(3)216-22
  • Burns JL, Emerson J, Kuypers J, Campbell AP, Gibson RL, McNamara S, Worrell K, Englund JA
    Respiratory viruses in children with cystic fibrosis: viral detection and clinical findings.
    Influenza and other respiratory viruses , 2012 May : 6(3)218-23
  • Knowles MR, Leigh MW, Carson JL, Davis SD, Dell SD, Ferkol TW, Olivier KN, Sagel SD, Rosenfeld M, Burns KA, Minnix SL, Armstrong MC, Lori A, Hazucha MJ, Loges NT, Olbrich H, Becker-Heck A, Schmidts M, Werner C, Omran H, Zariwala MA, Genetic Disorders of Mucociliary Clearance Consortium
    Mutations of DNAH11 in patients with primary ciliary dyskinesia with normal ciliary ultrastructure.
    Thorax , 2012 May : 67(5)433-41
  • Lopez-Guisa JM, Powers C, File D, Cochrane E, Jimenez N, Debley JS
    Airway epithelial cells from asthmatic children differentially express proremodeling factors.
    The Journal of allergy and clinical immunology , 2012 Apr, : 129(4)990-7.e6
  • Wilfond BS, Diekema DS
    Engaging children in genomics research: decoding the meaning of assent in research.
    Genetics in medicine : official journal of the American College of Medical Genetics , 2012 Apr, : 14(4)437-43
  • Wolf SM, Crock BN, Van Ness B, Lawrenz F, Kahn JP, Beskow LM, Cho MK, Christman MF, Green RC, Hall R, Illes J, Keane M, Knoppers BM, Koenig BA, Kohane IS, Leroy B, Maschke KJ, McGeveran W, Ossorio P, Parker LS, Petersen GM, Richardson HS, Scott JA, Terry SF, Wilfond BS, Wolf WA
    Managing incidental findings and research results in genomic research involving biobanks and archived data sets.
    Genetics in medicine : official journal of the American College of Medical Genetics , 2012 Apr, : 14(4)361-84
  • Mayer-Hamblett N, Kronmal RA, Gibson RL, Rosenfeld M, Retsch-Bogart G, Treggiari MM, Burns JL, Khan U, Ramsey BW, EPIC Investigators
    Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis.
    Pediatric pulmonology , 2012 Feb. : 47(2)125-34
  • Mayer-Hamblett N, Kronmal RA, Gibson RL, Rosenfeld M, Retsch-Bogart G, Treggiari MM, Burns JL, Khan U, Ramsey BW, EPIC Investigators
    Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis.
    Pediatric pulmonology , 2012 Feb. : 47(2)125-34
  • Mayer-Hamblett N, Kronmal RA, Gibson RL, Rosenfeld M, Retsch-Bogart G, Treggiari MM, Burns JL, Khan U, Ramsey BW, for the EPIC Investigators
    Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis.
    Pediatric pulmonology , 2012 Feb. : 125-134
  • Mayer-Hamblett N, Kronmal RA, Gibson RL, Rosenfeld M, Retsch-Bogart G, Treggiari MM, Burns JL, Khan U, Ramsey BW, EPIC Investigators
    Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis.
    Pediatric pulmonology , 2012 Feb. : 47(2)125-34
  • Mayer-Hamblett N, Kronmal RA, Gibson RL, Rosenfeld M, Retsch-Bogart G, Treggiari MM, Burns JL, Khan U, Ramsey BW, EPIC Investigators
    Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis.
    Pediatric pulmonology , 2012 Feb. : 47(2)125-34
  • Bronchiectasis
    Kendig and Chernicks Disorders of the Respiratory Tract in Children (8th Edition) , 2012 : 473-488
  • Chest Wall and Respiratory Muscle Disorders
    Kendig and Chernicks Disorders of the Respiratory Tract in Children (8th Edition) , 2012 : 631-646
  • Pulmonary Measurements
    AOSpine Measurements in Spine Care , 2012
  • The challenges of replicating the methodology between Phases I and III of the ISAAC programme
    Int J Tuberc Lung Dis , 2012 : 16(5)687-693
  • Correlating Haller index and cardiopulmonary disease in pectus excavatum
    Am J Surg , 2012 : 203(5)660-664
  • Changes over time in the relationship between symptoms of asthma, rhinoconjunctivitis and eczema. A global perspective from the International Study of Asthma and Allergies in Childhood (ISAAC)
    Allergol Immunopathol (Madr) , 2012 : 40(5)267-274
  • Satellite-based estimates of ambient air pollution and global variations in childhood asthma
    Environ Health Perspect , 2012 : 120(9)1333-1339
  • Simon TD, Whitlock KB, Riva-Cambrin J, Kestle JR, Rosenfeld M, Dean JM, Holubkov R, Langley M, Mayer-Hamblett N
    Association of intraventricular hemorrhage secondary to prematurity with cerebrospinal fluid shunt surgery in the first year following initial shunt placement.
    Journal of Neurosurgery. Pediatrics , 2012 Jan. : 54-63
  • Quon BS, Mayer-Hamblett N, Aitken ML, Goss CH
    Risk of Post Lung Transplant Renal Dysfunction in Adults with Cystic Fibrosis.
    Chest , 2012 Jan.
  • Pediatric Pulmonary Diseases and Cystic Fibrosis
    University of Washington School of Medicine Human Biology Course 541 Syllabu , 2012 : Course Director, Andrew Luks
  • Association of intraventricular hemorrhage secondary to prematurity with cerebrospinal fluid shunt surgery in the first year following initial shunt placement
    J Neurosurg Pediatr. , 2012 Jan. : 54-63
  • Rogers GB, Hoffman LR, Döring G
    Novel concepts in evaluating antimicrobial therapy for bacterial lung infections in patients with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2011 Dec. : 10(6)387-400
  • Knowles MR, Leigh MW, Carson JL, Davis SD, Dell SD, Ferkol TW, Olivier KN, Sagel SD, Rosenfeld M, Burns KA, Minnix SL, Armstrong MC, Lori A, Hazucha MJ, Loges NT, Olbrich H, Becker-Heck A, Schmidts M, Werner C, Omran H, Zariwala MA, for the Genetic Disorders of Mucociliary Clearance Consortium
    Mutations of DNAH11 in patients with primary ciliary dyskinesia with normal ciliary ultrastructure.
    Thorax , 2011 Dec.
  • Beskow LM, Namey EE, Cadigan RJ, Brazg T, Crouch J, Henderson GE, Michie M, Nelson DK, Tabor HK, Wilfond BS
    Research participants' perspectives on genotype-driven research recruitment.
    Journal of empirical research on human research ethics : JERHRE , 2011 Dec. : 6(4)3-20
  • Tabor HK, Brazg T, Crouch J, Namey EE, Fullerton SM, Beskow LM, Wilfond BS
    Parent perspectives on pediatric genetic research and implications for genotype-driven research recruitment.
    Journal of empirical research on human research ethics : JERHRE , 2011 Dec. : 6(4)41-52
  • Quon BS, Mayer-Hamblett N, Aitken ML, Smyth AR, Goss CH
    Risk factors for chronic kidney disease in adults with cystic fibrosis.
    American journal of respiratory and critical care medicine , 2011 Nov. : 1147-52
  • Kerby GS, Rosenfeld M, Ren CL, Mayer OH, Brumback L, Castile R, Hart MA, Hiatt P, Kloster M, Johnson R, Jones P, Davis SD
    Lung function distinguishes preschool children with CF from healthy controls in a multi-center setting.
    Pediatric pulmonology , 2011 Nov.
  • Ren CL, Rosenfeld M, Mayer OH, Davis SD, Kloster M, Castile RG, Hiatt PW, Hart M, Johnson R, Jones P, Brumback LC, Kerby GS
    Analysis of the associations between lung function and clinical features in preschool children with cystic fibrosis.
    Pediatric pulmonology , 2011 Nov.
  • Tarini BA, Tercyak KP, Wilfond BS
    Commentary: Children and predictive genomic testing: disease prevention, research protection, and our future.
    Journal of pediatric psychology , 2011 Nov. : 36(10)1113-21
  • Ghosh PS, Taute CT, Ghosh D
    Teaching NeuroImages: platybasia and basilar invagination in osteogenesis imperfecta.
    Neurology , 2011 Nov. 1 : 77(18)e108
  • Oermann CM, McCoy KS, Retsch-Bogart GZ, Gibson RL, McKevitt M, Montgomery AB
    Pseudomonas aeruginosa antibiotic susceptibility during long-term use of aztreonam for inhalation solution (AZLI).
    The Journal of antimicrobial chemotherapy , 2011 Oct. : 66(10)2398-404
  • Parental Requests for Interventions in Children With Lethal Conditions in Clinical Ethics in Pediatrics: A Case Based Textbook
    Cambridge University Press , 2011 Oct. : 174-180
  • Response to the Commentary: Children and Predictive Genomic Testing
    J Pediatr Psychol , 2011 Sept. 9 : 36(10)1128-9
  • Treggiari MM, Retsch-Bogart G, Mayer-Hamblett N, Khan U, Kulich M, Kronmal R, Williams J, Hiatt P, Gibson RL, Spencer T, Orenstein D, Chatfield BA, Froh DK, Burns JL, Rosenfeld M, Ramsey BW, Early Pseudomonas Infection Control (EPIC) Investigators
    Comparative efficacy and safety of 4 randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis.
    Archives of pediatrics & adolescent medicine , 2011 Sept. : 165(9)847-56
  • Treggiari MM, Retsch-Bogart G, Mayer-Hamblett N, Khan U, Kulich M, Kronmal R, Williams J, Hiatt P, Gibson RL, Spencer T, Orenstein D, Chatfield BA, Froh DK, Burns JL, Rosenfeld M, Ramsey BW, Early Pseudomonas Infection Control (EPIC) Investigators
    Comparative efficacy and safety of 4 randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis.
    Archives of pediatrics & adolescent medicine , 2011 Sept. : 847-56
  • Tuan TJ, Thorell EA, Hamblett NM, Kestle JR, Rosenfeld M, Simon TD
    Treatment and microbiology of repeated cerebrospinal fluid shunt infections in children.
    The Pediatric infectious disease journal , 2011 Sept. : 731-5
  • Stressmann FA, Rogers GB, Marsh P, Lilley AK, Daniels TW, Carroll MP, Hoffman LR, Jones G, Allen CE, Patel N, Forbes B, Tuck A, Bruce KD
    Does bacterial density in cystic fibrosis sputum increase prior to pulmonary exacerbation?
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2011 Sept. : 10(5)357-65
  • Tuan TJ, Thorell EA, Hamblett NM, Kestle JR, Rosenfeld M, Simon TD
    Treatment and microbiology of repeated cerebrospinal fluid shunt infections in children.
    The Pediatric infectious disease journal , 2011 Sept. : 731-5
  • Treggiari MM, Retsch-Bogart G, Mayer-Hamblett N, Khan U, Kulich M, Kronmal R, Williams J, Hiatt P, Gibson RL, Spencer T, Orenstein D, Chatfield BA, Froh DK, Burns JL, Rosenfeld M, Ramsey BW, Early Pseudomonas Infection Control (EPIC) Investigators
    Comparative efficacy and safety of 4 randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis.
    Archives of pediatrics & adolescent medicine , 2011 Sept. : 847-56
  • The Power of Knowledge: How Carrier and Prenatal Screening Altered the Clinical Goals of Genetic Testing in Achieving Justice in Genome Translation: Rethinking the Pathway to Benefit
    Oxford University Press , 2011 Sept.
  • Renaud C, Kuypers J, Aspesberro F, Rosenfeld M, Englund JA
    Emergence of oseltamivir-resistant pandemic H1N1 in an immunocompetent child with severe status asthmaticus.
    The Journal of asthma : official journal of the Association for the Care of Asthma , 2011 Aug. : 572-5
  • Mayer-Hamblett N, Kronmal RA, Gibson RL, Rosenfeld M, Retsch-Bogart G, Treggiari MM, Burns JL, Khan U, Ramsey BW, for the EPIC Investigators
    Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis.
    Pediatric pulmonology , 2011 Aug.
  • Population Carrier Screening: Psychological Impact
    Wiley & Sons , 2011 July 15 : eLS
  • Wainwright CE, Quittner AL, Geller DE, Nakamura C, Wooldridge JL, Gibson RL, Lewis S, Montgomery AB
    Aztreonam for inhalation solution (AZLI) in patients with cystic fibrosis, mild lung impairment, and P. aeruginosa.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2011 July : 10(4)234-42
  • Green N, Burns JL, Mayer-Hamblett N, Kloster M, Lands LC, Anstead M, Ratjen F, Saiman L
    Lack of association of small-colony-variant Staphylococcus aureus strains with long-term use of azithromycin in patients with cystic fibrosis.
    Journal of clinical microbiology , 2011 July : 2772-3
  • Rosenfeld M, Davis S, Brumback L, Daniel S, Rowbotham R, Johnson R, McNamara S, Jensen R, Barlow C, Ratjen F
    Inhaled hypertonic saline in infants and toddlers with cystic fibrosis: short-term tolerability, adherence, and safety.
    Pediatric pulmonology , 2011 July : 666-71
  • Loeve M, Gerbrands K, Hop WC, Rosenfeld M, Hartmann IC, Tiddens HA
    Bronchiectasis and pulmonary exacerbations in children and young adults with cystic fibrosis.
    Chest , 2011 July : 178-85
  • Update on treatment of childhood bronchiectasis unrelated to cystic-fibrosis.
    Paediatric respiratory reviews , 2011 June : 12(2)119-23
  • Akbarnia BA, Campbell RM, Dimeglio A, Flynn JM, Redding GJ, Sponseller PD, Vitale MG, Yazici M
    Fusionless procedures for the management of early-onset spine deformities in 2011: what do we know?
    Journal of children's orthopaedics , 2011 June : 5(3)159-72
  • Bastarache JA, Ong T, Matthay MA, Ware LB
    Alveolar fluid clearance is faster in women with acute lung injury compared to men.
    Journal of critical care , 2011 June : 26(3)249-56
  • Redding GJ, Mayer OH
    Structure-respiration function relationships before and after surgical treatment of early-onset scoliosis.
    Clinical orthopaedics and related research , 2011 May : 469(5)1330-4
  • Tercyak KP, Hensley Alford S, Emmons KM, Lipkus IM, Wilfond BS, McBride CM
    Parents' attitudes toward pediatric genetic testing for common disease risk.
    Pediatrics , 2011 May : 127(5)e1288-95
  • Sanders DB, Bittner RC, Rosenfeld M, Redding GJ, Goss CH
    Pulmonary exacerbations are associated with subsequent FEV1 decline in both adults and children with cystic fibrosis.
    Pediatric pulmonology , 2011 Apr, : 46(4)393-400
  • Ettinger RE, Hopper RA, Sandercoe G, Kifle Y, Saltzman B, Chen M, Perkins J
    Quantitative computed tomographic scan and polysomnographic analysis of patients with syndromic midface hypoplasia before and after Le Fort III distraction advancement.
    Plastic and reconstructive surgery , 2011 Apr, : 127(4)1612-9
  • Sanders DB, Bittner RC, Rosenfeld M, Redding GJ, Goss CH
    Pulmonary exacerbations are associated with subsequent FEV1 decline in both adults and children with cystic fibrosis.
    Pediatric pulmonology , 2011 Apr, : 393-400
  • Richer J, Ghebremichael MS, Chudley AE, Robinson WM, Wilfond BS, Solomon MZ
    Research use of leftover newborn bloodspots: attitudes of Canadian geneticists regarding storage and informed consent requirements.
    Genetics in medicine : official journal of the American College of Medical Genetics , 2011 Apr, : 13(4)305-13
  • Striegl AM, Redding GJ, Diblasi R, Crotwell D, Salyer J, Carter ER
    Use of a lung model to assess mechanical in-exsufflator therapy in infants with tracheostomy.
    Pediatric pulmonology , 2011 Mar. : 46(3)211-7
  • Rogers GB, Hoffman LR, Johnson MW, Mayer-Hamblett N, Schwarze J, Carroll MP, Bruce KD
    Using bacterial biomarkers to identify early indicators of cystic fibrosis pulmonary exacerbation onset.
    Expert review of molecular diagnostics , 2011 Mar. : 197-206
  • Rogers GB, Hoffman LR, Johnson MW, Mayer-Hamblett N, Schwarze J, Carroll MP, Bruce KD
    Using bacterial biomarkers to identify early indicators of cystic fibrosis pulmonary exacerbation onset.
    Expert review of molecular diagnostics , 2011 Mar. : 11(2)197-206
  • Striegl AM, Redding GJ, Diblasi R, Crotwell D, Salyer J, Carter ER
    Use of a lung model to assess mechanical in-exsufflator therapy in infants with tracheostomy.
    Pediatric pulmonology , 2011 Mar. : 46(3)211-7
  • Moskowitz SM, Emerson JC, McNamara S, Shell RD, Orenstein DM, Rosenbluth D, Katz MF, Ahrens R, Hornick D, Joseph PM, Gibson RL, Aitken ML, Benton WW, Burns JL
    Randomized trial of biofilm testing to select antibiotics for cystic fibrosis airway infection.
    Pediatric pulmonology , 2011 Feb. : 46(2)184-92
  • Structure-respiration function relationships before and after surgical treatment of early-onset scoliosis
    Clin Ortho Relat Res , 2011 : 469(4)1330-1334
  • Thoracic Insufficiency Syndrome
    The Growing Spine. Management of Spinal Disorders in Young Children , 2011
  • Pulmonary function testing in children with restrictive chest wall disorders
    Pediatric Allergy, Immunology, and Pulmonology , 2011 : 24(2)89-94
  • Sleep Disturbances
    Bermans Pediatric Decision Making , 2011 : Fifth Edition530-536
  • Debley JS, Ohanian AS, Spiekerman CF, Aitken ML, Hallstrand TS
    Effects of bronchoconstriction, minute ventilation, and deep inspiration on the composition of exhaled breath condensate.
    Chest , 2011 Jan. : 139(1)16-22
  • Open-label, Follow-On Study to Assess Continued Efficacy and Safety of Azithromycin in Children and Adolescents with CF Uninfected with Pseudomonas aeruginosa.
    Pediatric Pulmonology (In press) , 2011
  • A change in the pediatric leadership landscape
    Pain Med , 2011 : 121-7
  • The Respiratory System: Respiratory System Assessment
    Nelsons Essentials of Pediatrics, Sixth Edition , 2011
  • The Respiratory System: Control of Breathing
    Nelsons Essentials of Pediatrics, Sixth Edition , 2011
  • The Respiratory System: Upper Airway Obstruction
    Nelsons Essentials of Pediatrics, Sixth Edition , 2011
  • The Respiratory System: Lower Airway, Parenchymal, and
    Nelsons Essentials of Pediatrics, Sixth Edition , 2011
  • The Respiratory System: Cystic Fibrosis
    Nelsons Essentials of Pediatrics, Sixth Edition , 2011
  • The Respiratory System: Chest Wall and Pleura
    Nelsons Essentials of Pediatrics, Sixth Edition , 2011
  • What can we learn from first-year medical students perceptions of pain in the primary care setting?
    Pain Med , 2011 : 121-7
  • Olin JT, Burns K, Carson JL, Metjian H, Atkinson JJ, Davis SD, Dell SD, Ferkol TW, Milla CE, Olivier KN, Rosenfeld M, Baker B, Leigh MW, Knowles MR, Sagel SD, for the Genetic Disorders of Mucociliary Clearance Consortium
    Diagnostic yield of nasal scrape biopsies in primary ciliary dyskinesia: A multicenter experience.
    Pediatric pulmonology , 2011 Jan.
  • Quantitative Computed Tomographic Scan and Polysomnographic Analysis of Patients with Syndromic Midface Hypoplasia, before and after LeFort III Distraction Advancement
    Plastic Reconstr Surg , 2011 : 127(4)1612-9
  • Growth Attenuation: Health Outcomes and Social Services
    Hastings Center Report , 2011 : 41(5)7-8
  • Patient Perspectives on Group Benefits and Harms in Genetic Research
    Public Health Genomics , 2011 : 14(3)135-42
  • Myers RE, Manne SL, Wilfond B, Sifri R, Ziring B, Wolf TA, Cocroft J, Ueland A, Petrich A, Swan H, DiCarlo M, Weinberg DS
    A randomized trial of genetic and environmental risk assessment (GERA) for colorectal cancer risk in primary care: trial design and baseline findings.
    Contemporary clinical trials , 2011 Jan. : 32(1)25-31
  • Pediatric Neurology
    Ultimate Review for the Neurology Boards , 2011 : Chapter 12149-160
  • Ohanian AS, Zimmerman J, Debley JS
    Effects of sample processing, time and storage condition on cysteinyl leukotrienes in exhaled breath condensate.
    Journal of breath research , 2010 Dec. : 4(4)046002
  • Davis SD, Rosenfeld M, Kerby GS, Brumback L, Kloster MH, Acton JD, Colin AA, Conrad CK, Hart MA, Hiatt PW, Mogayzel PJ, Johnson RC, Wilcox SL, Castile RG
    Multicenter evaluation of infant lung function tests as cystic fibrosis clinical trial endpoints.
    American journal of respiratory and critical care medicine , 2010 Dec. : 1387-97
  • Oermann CM, Retsch-Bogart GZ, Quittner AL, Gibson RL, McCoy KS, Montgomery AB, Cooper PJ
    An 18-month study of the safety and efficacy of repeated courses of inhaled aztreonam lysine in cystic fibrosis.
    Pediatric pulmonology , 2010 Nov. : 45(11)1121-34
  • Accurso FJ, Rowe SM, Clancy JP, Boyle MP, Dunitz JM, Durie PR, Sagel SD, Hornick DB, Konstan MW, Donaldson SH, Moss RB, Pilewski JM, Rubenstein RC, Uluer AZ, Aitken ML, Freedman SD, Rose LM, Mayer-Hamblett N, Dong Q, Zha J, Stone AJ, Olson ER, Ordoñez CL, Campbell PW, Ashlock MA, Ramsey BW
    Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation.
    The New England journal of medicine , 2010 Nov. : 1991-2003
  • Striegl AM, Redding GJ, Diblasi R, Crotwell D, Salyer J, Carter ER
    Use of a lung model to assess mechanical in-exsufflator therapy in infants with tracheostomy.
    Pediatric pulmonology , 2010 Oct. 20
  • Solomon GM, Konstan MW, Wilschanski M, Billings J, Sermet-Gaudelus I, Accurso F, Vermeulen F, Levin E, Hathorne H, Reeves G, Sabbatini G, Hill A, Mayer-Hamblett N, Ashlock M, Clancy JP, Rowe SM
    An international randomized multicenter comparison of nasal potential difference techniques.
    Chest , 2010 Oct. : 919-28
  • Sanders DB, Bittner RC, Rosenfeld M, Hoffman LR, Redding GJ, Goss CH
    Failure to recover to baseline pulmonary function after cystic fibrosis pulmonary exacerbation.
    American journal of respiratory and critical care medicine , 2010 Sept. 1 : 182(5)627-32
  • Rosenfeld M, Emerson J, McNamara S, Joubran K, Retsch-Bogart G, Graff GR, Gutierrez HH, Kanga JF, Lahiri T, Noyes B, Ramsey B, Ren CL, Schechter M, Morgan W, Gibson RL
    Baseline characteristics and factors associated with nutritional and pulmonary status at enrollment in the cystic fibrosis EPIC observational cohort.
    Pediatric pulmonology , 2010 Sept. : 934-44
  • Rosenfeld M, Emerson J, McNamara S, Joubran K, Retsch-Bogart G, Graff GR, Gutierrez HH, Kanga JF, Lahiri T, Noyes B, Ramsey B, Ren CL, Schechter M, Morgan W, Gibson RL, EPIC Study Group Participating Clinical Sites
    Baseline characteristics and factors associated with nutritional and pulmonary status at enrollment in the cystic fibrosis EPIC observational cohort.
    Pediatric pulmonology , 2010 Sept. : 45(9)934-44
  • Sanders DB, Bittner RC, Rosenfeld M, Hoffman LR, Redding GJ, Goss CH
    Failure to recover to baseline pulmonary function after cystic fibrosis pulmonary exacerbation.
    American journal of respiratory and critical care medicine , 2010 Sept. 1 : 182(5)627-32
  • Ong T, McClintock DE, Kallet RH, Ware LB, Matthay MA, Liu KD
    Ratio of angiopoietin-2 to angiopoietin-1 as a predictor of mortality in acute lung injury patients.
    Critical care medicine , 2010 Sept. : 1845-51
  • Sanders DB, Bittner RC, Rosenfeld M, Hoffman LR, Redding GJ, Goss CH
    Failure to recover to baseline pulmonary function after cystic fibrosis pulmonary exacerbation.
    American journal of respiratory and critical care medicine , 2010 Sept. : 627-32
  • Rosenfeld M, Emerson J, McNamara S, Joubran K, Retsch-Bogart G, Graff GR, Gutierrez HH, Kanga JF, Lahiri T, Noyes B, Ramsey B, Ren CL, Schechter M, Morgan W, Gibson RL
    Baseline characteristics and factors associated with nutritional and pulmonary status at enrollment in the cystic fibrosis EPIC observational cohort.
    Pediatric pulmonology , 2010 Sept. : 934-44
  • Diblasi RM, Zignego JC, Smith CV, Hansen TN, Richardson CP
    Effective gas exchange in paralyzed juvenile rabbits using simple, inexpensive respiratory support devices.
    Pediatric research , 2010 Sept. 1
  • Bastarache JA, Ong T, Matthay MA, Ware LB
    Alveolar fluid clearance is faster in women with acute lung injury compared to men.
    Journal of critical care , 2010 Aug. 3
  • Rogers GB, Hoffman LR, Whiteley M, Daniels TW, Carroll MP, Bruce KD
    Revealing the dynamics of polymicrobial infections: implications for antibiotic therapy.
    Trends in microbiology , 2010 Aug. : 18(8)357-64
  • Elliott D, Burns JL, Hoffman LR
    Exploratory study of the prevalence and clinical significance of tobramycin-mediated biofilm induction in Pseudomonas aeruginosa isolates from cystic fibrosis patients.
    Antimicrobial agents and chemotherapy , 2010 July : 54(7)3024-6
  • Christen M, Kulasekara HD, Christen B, Kulasekara BR, Hoffman LR, Miller SI
    Asymmetrical distribution of the second messenger c-di-GMP upon bacterial cell division.
    Science (New York, N.Y.) , 2010 June 4 : 328(5983)1295-7
  • Debley JS, Stamey DC, Cochrane ES, Gama KL, Redding GJ
    Exhaled nitric oxide, lung function, and exacerbations in wheezy infants and toddlers.
    The Journal of allergy and clinical immunology , 2010 June : 125(6)1228-1234.e13
  • Debley JS, Stamey DC, Cochrane ES, Gama KL, Redding GJ
    Exhaled nitric oxide, lung function, and exacerbations in wheezy infants and toddlers.
    The Journal of allergy and clinical immunology , 2010 June : 125(6)1228-1234.e13
  • Diblasi RM, Zignego JC, Tang DM, Hildebrandt J, Smith CV, Hansen TN, Richardson CP
    Noninvasive respiratory support of juvenile rabbits by high-amplitude bubble continuous positive airway pressure.
    Pediatric research , 2010 June : 624-9
  • Striegl A, Chen ML, Kifle Y, Song K, Redding G
    Sleep-disordered breathing in children with thoracic insufficiency syndrome.
    Pediatric pulmonology , 2010 May : 45(5)469-74
  • Carter E, Waldhausen J, Zhang W, Hoffman L, Redding G
    Management of children with empyema: Pleural drainage is not always necessary.
    Pediatric pulmonology , 2010 May : 45(5)475-80
  • Striegl A, Chen ML, Kifle Y, Song K, Redding G
    Sleep-disordered breathing in children with thoracic insufficiency syndrome.
    Pediatric pulmonology , 2010 May : 45(5)469-74
  • Saiman L, Anstead M, Mayer-Hamblett N, Lands LC, Kloster M, Hocevar-Trnka J, Goss CH, Rose LM, Burns JL, Marshall BC, Ratjen F, AZ0004 Azithromycin Study Group
    Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa: a randomized controlled trial.
    JAMA : the journal of the American Medical Association , 2010 May : 1707-15
  • Carter E, Waldhausen J, Zhang W, Hoffman L, Redding G
    Management of children with empyema: Pleural drainage is not always necessary.
    Pediatric pulmonology , 2010 May : 45(5)475-80
  • DiBlasi RM, Crotwell D, Geiduscheck JM, Richardson P, Smith A, Salyer JW, Rosenfeld M
    Therapeutic bilateral lung lavage in a child with pulmonary alveolar proteinosis.
    Pediatric critical care medicine : a journal of the Society of Critical Care Medicine and the World Federation of Pediatric Intensive and Critical Care Societies , 2010 May : e28-31
  • Striegl A, Chen ML, Kifle Y, Song K, Redding G
    Sleep-disordered breathing in children with thoracic insufficiency syndrome.
    Pediatric pulmonology , 2010 May : 469-74
  • Striegl A, Chen ML, Kifle Y, Song K, Redding G
    Sleep-disordered breathing in children with thoracic insufficiency syndrome.
    Pediatric pulmonology , 2010 May : 469-74
  • Emerson J, McNamara S, Buccat AM, Worrell K, Burns JL
    Changes in cystic fibrosis sputum microbiology in the United States between 1995 and 2008.
    Pediatric pulmonology , 2010 Apr, : 363-70
  • Rogers GB, Carroll MP, Hoffman LR, Walker AW, Fine DA, Bruce KD
    Comparing the microbiota of the cystic fibrosis lung and human gut.
    Gut microbes , 2010 Mar. : 1(2)85-93
  • Sanders DB, Hoffman LR, Emerson J, Gibson RL, Rosenfeld M, Redding GJ, Goss CH
    Return of FEV1 after pulmonary exacerbation in children with cystic fibrosis.
    Pediatric pulmonology , 2010 Feb. : 45(2)127-34
  • Sanders DB, Hoffman LR, Emerson J, Gibson RL, Rosenfeld M, Redding GJ, Goss CH
    Return of FEV1 after pulmonary exacerbation in children with cystic fibrosis.
    Pediatric pulmonology , 2010 Feb. : 127-34
  • Sanders DB, Hoffman LR, Emerson J, Gibson RL, Rosenfeld M, Redding GJ, Goss CH
    Return of FEV1 after pulmonary exacerbation in children with cystic fibrosis.
    Pediatric pulmonology , 2010 Feb. : 45(2)127-34
  • Sanders DB, Hoffman LR, Emerson J, Gibson RL, Rosenfeld M, Redding GJ, Goss CH
    Return of FEV1 after pulmonary exacerbation in children with cystic fibrosis.
    Pediatric pulmonology , 2010 Feb. : 45(2)127-34
  • Sanders DB, Hoffman LR, Emerson J, Gibson RL, Rosenfeld M, Redding GJ, Goss CH
    Return of FEV1 after pulmonary exacerbation in children with cystic fibrosis.
    Pediatric pulmonology , 2010 Feb. : 127-34
  • Tiddens HA, Donaldson SH, Rosenfeld M, Paré PD
    Cystic fibrosis lung disease starts in the small airways: can we treat it more effectively?
    Pediatric pulmonology , 2010 Feb. : 107-17
  • Hoffman LR, Richardson AR, Houston LS, Kulasekara HD, Martens-Habbena W, Klausen M, Burns JL, Stahl DA, Hassett DJ, Fang FC, Miller SI
    Nutrient availability as a mechanism for selection of antibiotic tolerant Pseudomonas aeruginosa within the CF airway.
    PLoS pathogens , 2010 Jan. 8 : 6(1)e1000712
  • Thoracic Insufficiency: Pulmonary Pathophysiology
    Growing Spine: Management of Spinal Disorders in the Young Child , 2010
  • New therapies for chest wall and spine disorders in children
    Paediatric Respiratory Reviews , 2010 : 11(1)S15-16
  • Childhood bronchiectasis around the world
    Paediatric Respiratory Reviews , 2010 : 11(1)S73
  • Congenital Lung Malformations
    ACCP/APP Pediatric Pulmonary Board Review: 1st Edition , 2010 : 1169-174
  • Disorders of the Chest Wall, Diaphragm, and Pleural and Mediastinal Spaces
    ACCP/APP Pediatric Pulmonary Board Review: 1st Edition , 2010 : 1127-134
  • Ambient particulate pollution and the world-wide prevalence of asthma, rhinoconjunctivitis and eczema in children: Phase One of the International Study of Asthma and Allergies in Childhood (ISAAC)
    Occup Environ , 2010 : 67(5)293-300
  • Which population level environmental factors are associated with asthma, rhinoconjunctivitis and eczema? Review of the cological analyses of ISAAC Phase One
    Respir Res , 2010 : 11(8)
  • Is pediatric pulmonary research training in dire straits.
    Pediatric pulmonology , 2010 Jan. : 45(1)34-5
  • The impact of the method of consent on response rates in the ISAAC time trends study
    Int J Tuberc Lung Dis , 2010 : 14(8)938
  • Curriculum management and governance structure
    Acad Med , 2010 : 85(9)S593-S597
  • What are the pathologic and pathophysiologic changes that accompany ALI and ARDS?
    The Evidenced Based Practice of Critical Care Medicine , 2010 : Ed. Patrick Neligan and Clifford Deutschman.(Philadelphia: Saunders Elsevier)82-87
  • The Pulmonary System
    First Aid for the Pediatric Boards , 2010 : 2nd Edition. Ed. Tao Le(New York: McGraw-Hill)567-600
  • Pulmonary Exacerbations
    Lung Biology in Health and Disease: Cystic Fibrosis , 2010
  • Cystic Fibrosis" and "Bronchiectasis
    The Netter Collection of Medical Illustrations, 2nd Edition: The Respiratory System , 2010
  • Choroid Plexus Hypertrophy in a Child with Tetrasomy 9p
    Blackwell Publishing/American Society of Neuroimaging , 2010 : 101
  • Redding GJ, Byrnes CA
    Chronic respiratory symptoms and diseases among indigenous children.
    Pediatric clinics of North America , 2009 Dec. : 56(6)1323-42
  • Borowitz D, Robinson KA, Rosenfeld M, Davis SD, Sabadosa KA, Spear SL, Michel SH, Parad RB, White TB, Farrell PM, Marshall BC, Accurso FJ
    Cystic Fibrosis Foundation evidence-based guidelines for management of infants with cystic fibrosis.
    The Journal of pediatrics , 2009 Dec. : S73-93
  • Schechter MS, McColley SA, Silva S, Haselkorn T, Konstan MW, Wagener JS
    Association of socioeconomic status with the use of chronic therapies and healthcare utilization in children with cystic fibrosis.
    The Journal of pediatrics , 2009 Nov. : 634-9.e1-4
  • Ashlock MA, Beall RJ, Hamblett NM, Konstan MW, Penland CM, Ramsey BW, Van Dalfsen JM, Wetmore DR, Campbell PW 3rd
    A pipeline of therapies for cystic fibrosis.
    Seminars in respiratory and critical care medicine , 2009 Oct. : 611-26
  • Ashlock MA, Beall RJ, Hamblett NM, Konstan MW, Penland CM, Ramsey BW, Van Dalfsen JM, Wetmore DR, Campbell PW 3rd
    A pipeline of therapies for cystic fibrosis.
    Seminars in respiratory and critical care medicine , 2009 Oct. : 611-26
  • Bartlett JR, Friedman KJ, Ling SC, Pace RG, Bell SC, Bourke B, Castaldo G, Castellani C, Cipolli M, Colombo C, Colombo JL, Debray D, Fernandez A, Lacaille F, Macek M Jr, Rowland M, Salvatore F, Taylor CJ, Wainwright C, Wilschanski M, Zemková D, Hannah WB, Phillips MJ, Corey M, Zielenski J, Dorfman R, Wang Y, Zou F, Silverman LM, Drumm ML, Wright FA, Lange EM, Durie PR, Knowles MR, Gene Modifier Study Group
    Genetic modifiers of liver disease in cystic fibrosis.
    JAMA : the journal of the American Medical Association , 2009 Sept. 9 : 302(10)1076-83
  • Cloonan YK, Kifle Y, Davis S, Speltz ML, Werler MM, Starr JR
    Sleep outcomes in children with hemifacial microsomia and controls: a follow-up study.
    Pediatrics , 2009 Aug. : e313-21
  • Chaicharn J, Lin Z, Chen ML, Ward SL, Keens T, Khoo MC
    Model-based assessment of cardiovascular autonomic control in children with obstructive sleep apnea.
    Sleep , 2009 July : 32(7)927-38
  • Treggiari MM, Rosenfeld M, Mayer-Hamblett N, Retsch-Bogart G, Gibson RL, Williams J, Emerson J, Kronmal RA, Ramsey BW
    Early anti-pseudomonal acquisition in young patients with cystic fibrosis: rationale and design of the EPIC clinical trial and observational study'.
    Contemporary clinical trials , 2009 May : 256-68
  • Treggiari MM, Rosenfeld M, Mayer-Hamblett N, Retsch-Bogart G, Gibson RL, Williams J, Emerson J, Kronmal RA, Ramsey BW, EPIC Study Group
    Early anti-pseudomonal acquisition in young patients with cystic fibrosis: rationale and design of the EPIC clinical trial and observational study'.
    Contemporary clinical trials , 2009 May : 30(3)256-68
  • Retsch-Bogart GZ, Quittner AL, Gibson RL, Oermann CM, McCoy KS, Montgomery AB, Cooper PJ
    Efficacy and safety of inhaled aztreonam lysine for airway pseudomonas in cystic fibrosis.
    Chest , 2009 May : 135(5)1223-32
  • Treggiari MM, Rosenfeld M, Mayer-Hamblett N, Retsch-Bogart G, Gibson RL, Williams J, Emerson J, Kronmal RA, Ramsey BW, EPIC Study Group
    Early anti-pseudomonal acquisition in young patients with cystic fibrosis: rationale and design of the EPIC clinical trial and observational study'.
    Contemporary clinical trials , 2009 May : 256-68
  • Ong T, Stuart-Killion RB, Daniel BM, Presnell LB, Zhuo H, Matthay MA, Liu KD
    Higher pulmonary dead space may predict prolonged mechanical ventilation after cardiac surgery.
    Pediatric pulmonology , 2009 May : 457-63
  • Treggiari MM, Rosenfeld M, Mayer-Hamblett N, Retsch-Bogart G, Gibson RL, Williams J, Emerson J, Kronmal RA, Ramsey BW
    Early anti-pseudomonal acquisition in young patients with cystic fibrosis: rationale and design of the EPIC clinical trial and observational study'.
    Contemporary clinical trials , 2009 May : 256-68
  • Treggiari MM, Rosenfeld M, Mayer-Hamblett N, Retsch-Bogart G, Gibson RL, Williams J, Emerson J, Kronmal RA, Ramsey BW
    Early anti-pseudomonal acquisition in young patients with cystic fibrosis: rationale and design of the EPIC clinical trial and observational study'.
    Contemporary clinical trials , 2009 May : 256-68
  • Brannon MK, Davis JM, Mathias JR, Hall CJ, Emerson JC, Crosier PS, Huttenlocher A, Ramakrishnan L, Moskowitz SM
    Pseudomonas aeruginosa Type III secretion system interacts with phagocytes to modulate systemic infection of zebrafish embryos.
    Cellular microbiology , 2009 Feb. 6
  • Bronchiectasis in children.
    Pediatric clinics of North America , 2009 Feb. : 56(1)157-71
  • Sagel SD, Gibson RL, Emerson J, McNamara S, Burns JL, Wagener JS, Ramsey BW
    Impact of Pseudomonas and Staphylococcus infection on inflammation and clinical status in young children with cystic fibrosis.
    The Journal of pediatrics , 2009 Feb. : 183-8
  • Sagel SD, Gibson RL, Emerson J, McNamara S, Burns JL, Wagener JS, Ramsey BW, Inhaled Tobramycin in Young Children Study Group, Cystic Fibrosis Foundation Therapeutics Development Network
    Impact of Pseudomonas and Staphylococcus infection on inflammation and clinical status in young children with cystic fibrosis.
    The Journal of pediatrics , 2009 Feb. : 154(2)183-8
  • Sagel SD, Gibson RL, Emerson J, McNamara S, Burns JL, Wagener JS, Ramsey BW
    Impact of Pseudomonas and Staphylococcus infection on inflammation and clinical status in young children with cystic fibrosis.
    The Journal of pediatrics , 2009 Feb. : 183-8
  • Sagel SD, Gibson RL, Emerson J, McNamara S, Burns JL, Wagener JS, Ramsey BW
    Impact of Pseudomonas and Staphylococcus infection on inflammation and clinical status in young children with cystic fibrosis.
    The Journal of pediatrics , 2009 Feb. : 183-8
  • Evaluation of Chronic Therapy for Bronchiectais due to Cystic Fibrosis and Diseases unrelated to Cystic Fibrosis
    Pediatric Clinics of North America , 2009
  • Plan for Pediatric Respiratory Diseases Research: an NHLBI Working Group
    Pediatri Pulmonol , 2009 : 44(1)2-13
  • Respiratory Disorders
    Oxford American Handbook of Pediatrics , 2009
  • Translation of questions: the International Study of Asthma and Allergies in Childhood (ISAAC) experience
    Int J Tuberc Lung Dis , 2009 : 13(9)1174-1182
  • Burden of bronchiectasis in Indigenous peoples How can it be improved?
    Current Pediatric Reviews , 2009 : 5198-206
  • Mayer OH, Redding G
    Early changes in pulmonary function after vertical expandable prosthetic titanium rib insertion in children with thoracic insufficiency syndrome.
    Journal of pediatric orthopedics , 2009 Jan. : 29(1)35-8
  • A retrospective look at relationships amoung sleep variables and body mass index in children and adolescents
    Sleep , 2009 : 32 (abstract supplement): A105
  • Hsia D, DiBlasi RM, Richardson P, Crotwell D, Debley J, Carter E
    The effects of flexible bronchoscopy on mechanical ventilation in a pediatric lung model.
    Chest , 2009 Jan. : 135(1)33-40
  • Hoffman LR, Kulasekara HD, Emerson J, Houston LS, Burns JL, Ramsey BW, Miller SI
    Pseudomonas aeruginosa lasR mutants are associated with cystic fibrosis lung disease progression.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2009 Jan. : 66-70
  • Hoffman LR, Kulasekara HD, Emerson J, Houston LS, Burns JL, Ramsey BW, Miller SI
    Pseudomonas aeruginosa lasR mutants are associated with cystic fibrosis lung disease progression.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2009 Jan. : 8(1)66-70
  • Net Alveolar Fluid Clearance Is Faster in Women with Acute Lung Injury
    Am J Respir Crit Care Med , 2009 : 179A3380
  • Higher Angiopoietin-2 Is Associated with Mortality and Activated Endothelium in Acute Lung Injury.
    Am J Respir Crit Care Med , 2009 : 179A2498
  • Hoffman LR, Kulasekara HD, Emerson J, Houston LS, Burns JL, Ramsey BW, Miller SI
    Pseudomonas aeruginosa lasR mutants are associated with cystic fibrosis lung disease progression.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2009 Jan. : 66-70
  • Asthma
    Primary care of the child with a chronic condition (5th ed) , 2009 : P. Jackson and J. Vesseys(Philadelphia: Elsevier)
  • Respiratory Issues
    Oxford American Handbook of Pediatrics , 2009 : Stapleton FB, Tasker RC, McClure RJ, Acerini CL, editors(Oxford Press, New York, NY)
  • Moskowitz SM, Chmiel JF, Sternen DL, Cheng E, Gibson RL, Marshall SG, Cutting GR
    Clinical practice and genetic counseling for cystic fibrosis and CFTR-related disorders.
    Genetics in medicine : official journal of the American College of Medical Genetics , 2008 Dec. : 10(12)851-68
  • McCoy KS, Quittner AL, Oermann CM, Gibson RL, Retsch-Bogart GZ, Montgomery AB
    Inhaled aztreonam lysine for chronic airway Pseudomonas aeruginosa in cystic fibrosis.
    American journal of respiratory and critical care medicine , 2008 Nov. 1 : 178(9)921-8
  • Sanders DB, Rosenfeld M, Mayer-Hamblett N, Stamey D, Redding GJ
    Reproducibility of spirometry during cystic fibrosis pulmonary exacerbations.
    Pediatric pulmonology , 2008 Nov. : 1142-6
  • Sanders DB, Rosenfeld M, Mayer-Hamblett N, Stamey D, Redding GJ
    Reproducibility of spirometry during cystic fibrosis pulmonary exacerbations.
    Pediatric pulmonology , 2008 Nov. : 1142-6
  • DiBlasi RM, Salyer JW, Zignego JC, Redding GJ, Richardson CP
    The impact of imposed expiratory resistance in neonatal mechanical ventilation: a laboratory evaluation.
    Respiratory care , 2008 Nov. : 1450-60
  • Moskowitz SM, Silva SJ, Mayer-Hamblett N, Pasta DJ, Mink DR, Mabie JA, Konstan MW, Wagener JS, Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis (ESCF)
    Shifting patterns of inhaled antibiotic use in cystic fibrosis.
    Pediatric pulmonology , 2008 Sept. : 874-81
  • Striegl AM, Chen ML
    Response to Clinical Corners in Sleep Medicine: "Management of obstructive sleep apnea in patients with congenital heart disease and Fontan procedures" (Sleep Med 2007;8:537-8).
    Sleep medicine , 2008 July : 591-2
  • Striegl AM, Chen ML
    Response to Clinical Corners in Sleep Medicine: "Management of obstructive sleep apnea in patients with congenital heart disease and Fontan procedures" (Sleep Med 2007;8:537-8).
    Sleep medicine , 2008 July : 591-2
  • Hsieh T, Chen M, McAfee A, Kifle Y
    Sleep-related breathing disorder in children with vagal nerve stimulators.
    Pediatric neurology , 2008 Feb. : 99-103
  • Hsieh T, Chen M, McAfee A, Kifle Y
    Sleep-related breathing disorder in children with vagal nerve stimulators.
    Pediatric neurology , 2008 Feb. : 38(2)99-103
  • Retsch-Bogart GZ, Burns JL, Otto KL, Liou TG, McCoy K, Oermann C, Gibson RL, AZLI Phase II Study Group
    A phase 2 study of aztreonam lysine for inhalation to treat patients with cystic fibrosis and Pseudomonas aeruginosa infection.
    Pediatric pulmonology , 2008 Jan. : 43(1)47-58
  • Clinical practice and genetic counseling for cystic fibrosis and CFTR-related disorders
    Genet Med , 2008 : 10(12)851-868
  • Cystic Fibrosis: Respiratory Manifestations
    In Pediatric Respiratory Diseases , 2008
  • Debley JS, Hallstrand TS, Monge T, Ohanian A, Redding GJ, Zimmerman J
    Methods to improve measurement of cysteinyl leukotrienes in exhaled breath condensate from subjects with asthma and healthy controls.
    The Journal of allergy and clinical immunology , 2007 Nov. : 120(5)1216-7
  • Dovey M, Aitken ML, Emerson J, McNamara S, Waltz DA, Gibson RL
    Oral corticosteroid therapy in cystic fibrosis patients hospitalized for pulmonary exacerbation: a pilot study.
    Chest , 2007 Oct. : 1212-8
  • Ernst RK, Moskowitz SM, Emerson JC, Kraig GM, Adams KN, Harvey MD, Ramsey B, Speert DP, Burns JL, Miller SI
    Unique lipid a modifications in Pseudomonas aeruginosa isolated from the airways of patients with cystic fibrosis.
    The Journal of infectious diseases , 2007 Oct. 1 : 1088-92
  • Veenstra DL, Harris J, Gibson RL, Rosenfeld M, Burke W, Watts C
    Pharmacogenomic testing to prevent aminoglycoside-induced hearing loss in cystic fibrosis patients: potential impact on clinical, patient, and economic outcomes.
    Genetics in medicine : official journal of the American College of Medical Genetics , 2007 Oct. : 695-704
  • Treggiari MM, Rosenfeld M, Retsch-Bogart G, Gibson R, Ramsey B
    Approach to eradication of initial Pseudomonas aeruginosa infection in children with cystic fibrosis.
    Pediatric pulmonology , 2007 Sept. : 42(9)751-6
  • Treggiari MM, Rosenfeld M, Retsch-Bogart G, Gibson R, Ramsey B
    Approach to eradication of initial Pseudomonas aeruginosa infection in children with cystic fibrosis.
    Pediatric pulmonology , 2007 Sept. : 751-6
  • Treggiari MM, Rosenfeld M, Retsch-Bogart G, Gibson R, Ramsey B
    Approach to eradication of initial Pseudomonas aeruginosa infection in children with cystic fibrosis.
    Pediatric pulmonology , 2007 Sept. : 751-6
  • Deterding RR, Lavange LM, Engels JM, Mathews DW, Coquillette SJ, Brody AS, Millard SP, Ramsey BW
    Phase 2 randomized safety and efficacy trial of nebulized denufosol tetrasodium in cystic fibrosis.
    American journal of respiratory and critical care medicine , 2007 Aug. 15 : 362-9
  • Mayer-Hamblett N, Ramsey BW, Kronmal RA
    Advancing outcome measures for the new era of drug development in cystic fibrosis.
    Proceedings of the American Thoracic Society , 2007 Aug. : 370-7
  • Use of lung imaging studies as outcome measures for development of new therapies in cystic fibrosis.
    Proceedings of the American Thoracic Society , 2007 Aug. 1 : 359-63
  • Outcome measures for development of new therapies in cystic fibrosis: are we making progress and what are the next steps?
    Proceedings of the American Thoracic Society , 2007 Aug. 1 : 367-9
  • Mayer-Hamblett N, Ramsey BW, Kronmal RA
    Advancing outcome measures for the new era of drug development in cystic fibrosis.
    Proceedings of the American Thoracic Society , 2007 Aug. 1 : 370-7
  • An overview of endpoints for cystic fibrosis clinical trials: one size does not fit all.
    Proceedings of the American Thoracic Society , 2007 Aug. : 299-301
  • Davis SD, Brody AS, Emond MJ, Brumback LC, Rosenfeld M
    Endpoints for clinical trials in young children with cystic fibrosis.
    Proceedings of the American Thoracic Society , 2007 Aug. : 418-30
  • Gibson RL, Emerson J, Mayer-Hamblett N, Burns JL, McNamara S, Accurso FJ, Konstan MW, Chatfield BA, Retsch-Bogart G, Waltz DA, Acton J, Zeitlin P, Hiatt P, Moss R, Williams J, Ramsey BW
    Duration of treatment effect after tobramycin solution for inhalation in young children with cystic fibrosis.
    Pediatric pulmonology , 2007 July : 610-23
  • Clancy JP, Rowe SM, Bebok Z, Aitken ML, Gibson R, Zeitlin P, Berclaz P, Moss R, Knowles MR, Oster RA, Mayer-Hamblett N, Ramsey B
    No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations.
    American journal of respiratory cell and molecular biology , 2007 July : 37(1)57-66
  • Clancy JP, Rowe SM, Bebok Z, Aitken ML, Gibson R, Zeitlin P, Berclaz P, Moss R, Knowles MR, Oster RA, Mayer-Hamblett N, Ramsey B
    No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations.
    American journal of respiratory cell and molecular biology , 2007 July : 57-66
  • Gibson RL, Emerson J, Mayer-Hamblett N, Burns JL, McNamara S, Accurso FJ, Konstan MW, Chatfield BA, Retsch-Bogart G, Waltz DA, Acton J, Zeitlin P, Hiatt P, Moss R, Williams J, Ramsey BW
    Duration of treatment effect after tobramycin solution for inhalation in young children with cystic fibrosis.
    Pediatric pulmonology , 2007 July : 610-23
  • Clancy JP, Rowe SM, Bebok Z, Aitken ML, Gibson R, Zeitlin P, Berclaz P, Moss R, Knowles MR, Oster RA, Mayer-Hamblett N, Ramsey B
    No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations.
    American journal of respiratory cell and molecular biology , 2007 July : 57-66
  • Gibson RL, Emerson J, Mayer-Hamblett N, Burns JL, McNamara S, Accurso FJ, Konstan MW, Chatfield BA, Retsch-Bogart G, Waltz DA, Acton J, Zeitlin P, Hiatt P, Moss R, Williams J, Ramsey BW
    Duration of treatment effect after tobramycin solution for inhalation in young children with cystic fibrosis.
    Pediatric pulmonology , 2007 July : 610-23
  • Nguyen D, Emond MJ, Mayer-Hamblett N, Saiman L, Marshall BC, Burns JL
    Clinical response to azithromycin in cystic fibrosis correlates with in vitro effects on Pseudomonas aeruginosa phenotypes.
    Pediatric pulmonology , 2007 June : 533-41
  • Tablizo MA, Jacinto P, Parsley D, Chen ML, Ramanathan R, Keens TG
    Supine sleeping position does not cause clinical aspiration in neonates in hospital newborn nurseries.
    Archives of pediatrics & adolescent medicine , 2007 May : 507-10
  • Hallstrand TS, Debley JS, Farin FM, Henderson WR Jr
    Role of MUC5AC in the pathogenesis of exercise-induced bronchoconstriction.
    The Journal of allergy and clinical immunology , 2007 May : 119(5)1092-8
  • Heike CL, Avellino AM, Mirza SK, Kifle Y, Perkins J, Sze R, Egbert M, Hing AV
    Sleep disturbances in 22q11.2 deletion syndrome: a case with obstructive and central sleep apnea.
    The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association , 2007 May : 340-6
  • Mayer-Hamblett N, Aitken ML, Accurso FJ, Kronmal RA, Konstan MW, Burns JL, Sagel SD, Ramsey BW
    Association between pulmonary function and sputum biomarkers in cystic fibrosis.
    American journal of respiratory and critical care medicine , 2007 Apr, 15 : 822-8
  • Goss CH, Mayer-Hamblett N, Kronmal RA, Williams J, Ramsey BW
    Laboratory parameter profiles among patients with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2007 Apr, : 117-23
  • Mayer-Hamblett N, Aitken ML, Accurso FJ, Kronmal RA, Konstan MW, Burns JL, Sagel SD, Ramsey BW
    Association between pulmonary function and sputum biomarkers in cystic fibrosis.
    American journal of respiratory and critical care medicine , 2007 Apr, : 822-8
  • Goss CH, Mayer-Hamblett N, Kronmal RA, Williams J, Ramsey BW
    Laboratory parameter profiles among patients with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society , 2007 Apr, : 117-23
  • D'Argenio DA, Wu M, Hoffman LR, Kulasekara HD, Déziel E, Smith EE, Nguyen H, Ernst RK, Larson Freeman TJ, Spencer DH, Brittnacher M, Hayden HS, Selgrade S, Klausen M, Goodlett DR, Burns JL, Ramsey BW, Miller SI
    Growth phenotypes of Pseudomonas aeruginosa lasR mutants adapted to the airways of cystic fibrosis patients.
    Molecular microbiology , 2007 Apr, : 512-33
  • Comeau AM, Accurso FJ, White TB, Campbell PW 3rd, Hoffman G, Parad RB, Wilfond BS, Rosenfeld M, Sontag MK, Massie J, Farrell PM, O'Sullivan BP
    Guidelines for implementation of cystic fibrosis newborn screening programs: Cystic Fibrosis Foundation workshop report.
    Pediatrics , 2007 Feb. : e495-518
  • Carter ER, Debley JS, Redding GR
    Chronic productive cough in school children: prevalence and associations with asthma and environmental tobacco smoke exposure.
    Cough (London, England) , 2006 Dec. 27 : 211
  • Hoffman LR, Déziel E, D'Argenio DA, Lépine F, Emerson J, McNamara S, Gibson RL, Ramsey BW, Miller SI
    Selection for Staphylococcus aureus small-colony variants due to growth in the presence of Pseudomonas aeruginosa.
    Proceedings of the National Academy of Sciences of the United States of America , 2006 Dec. 26 : 19890-5
  • Hoffman LR, Déziel E, D'Argenio DA, Lépine F, Emerson J, McNamara S, Gibson RL, Ramsey BW, Miller SI
    Selection for Staphylococcus aureus small-colony variants due to growth in the presence of Pseudomonas aeruginosa.
    Proceedings of the National Academy of Sciences of the United States of America , 2006 Dec. 26 : 19890-5
  • Sucharew H, Goss CH, Millard SP, Ramsey BW
    Respiratory adverse event profiles in cystic fibrosis placebo subjects in short- and long-term inhaled therapy trials.
    Contemporary clinical trials , 2006 Dec. : 561-70
  • Grosse SD, Rosenfeld M, Devine OJ, Lai HJ, Farrell PM
    Potential impact of newborn screening for cystic fibrosis on child survival: a systematic review and analysis.
    The Journal of pediatrics , 2006 Sept. : 362-6
  • Appropriate compensation of pediatric research participants: thoughts from an Institute of Medicine committee report.
    The Journal of pediatrics , 2006 July : S15-9
  • Smith EE, Buckley DG, Wu Z, Saenphimmachak C, Hoffman LR, D'Argenio DA, Miller SI, Ramsey BW, Speert DP, Moskowitz SM, Burns JL, Kaul R, Olson MV
    Genetic adaptation by Pseudomonas aeruginosa to the airways of cystic fibrosis patients.
    Proceedings of the National Academy of Sciences of the United States of America , 2006 May 30 : 8487-92
  • Debley JS, Carter ER, Redding GJ
    Prevalence and impact of gastroesophageal reflux in adolescents with asthma: a population-based study.
    Pediatric pulmonology , 2006 May : 41(5)475-81
  • Halbert CL, Miller AD, McNamara S, Emerson J, Gibson RL, Ramsey B, Aitken ML
    Prevalence of neutralizing antibodies against adeno-associated virus (AAV) types 2, 5, and 6 in cystic fibrosis and normal populations: Implications for gene therapy using AAV vectors.
    Human gene therapy , 2006 Apr, : 440-7
  • Chen ML, Turkel SB, Jacobson JR, Keens TG
    Alcohol use in congenital central hypoventilation syndrome.
    Pediatric pulmonology , 2006 Mar. : 283-5
  • Ferkol T, Rosenfeld M, Milla CE
    Cystic fibrosis pulmonary exacerbations.
    The Journal of pediatrics , 2006 Feb. : 259-64
  • Congenital syndromes affecting respiratory control during sleep
    Sleep: a Comprehensive Handbook , 2006 : Chapter 66, pp517-527
  • The Respiratory System: Assessment
    Essentials of Pediatrics, Fifth Edition , 2006
  • The Respiratory System: Control of Breathing
    Essentials of Pediatrics, Fifth Edition , 2006
  • The Respiratory System: Upper Airway Obstruction
    Essentials of Pediatrics, Fifth Edition , 2006
  • Respiratory System: Lower Airway, Parenchymal, and Pulmonary Vascular Diseases
    Essentials of Pediatrics, Fifth Edition , 2006
  • The Respiratory System: Cystic Fibrosis
    Essentials of Pediatrics, Fifth Edition , 2006
  • The Respiratory System: Chest Wall and Pleura
    Essentials of Pediatrics, Fifth Edition , 2006
  • A new oral health elective for medical students at the University of Washington
    Teach Learn Med , 2006 : 18(4)336-342
  • Goss CH, Rubenfeld GD, Ramsey BW, Aitken ML
    Clinical trial participants compared with nonparticipants in cystic fibrosis.
    American journal of respiratory and critical care medicine , 2006 Jan. 1 : 98-104
  • Hendeles L, Marshik PL, Ahrens R, Kifle Y, Shuster J
    Response to nonprescription epinephrine inhaler during nocturnal asthma.
    Annals of allergy, asthma & immunology : official publication of the American College of Allergy, Asthma, & Immunology , 2005 Dec. : 530-4
  • Moskowitz SM, Foster JM, Emerson JC, Gibson RL, Burns JL
    Use of Pseudomonas biofilm susceptibilities to assign simulated antibiotic regimens for cystic fibrosis airway infection.
    The Journal of antimicrobial chemotherapy , 2005 Nov. : 879-86
  • Kulich M, Rosenfeld M, Campbell J, Kronmal R, Gibson RL, Goss CH, Ramsey B
    Disease-specific reference equations for lung function in patients with cystic fibrosis.
    American journal of respiratory and critical care medicine , 2005 Oct. 1 : 172(7)885-91
  • Kulich M, Rosenfeld M, Campbell J, Kronmal R, Gibson RL, Goss CH, Ramsey B
    Disease-specific reference equations for lung function in patients with cystic fibrosis.
    American journal of respiratory and critical care medicine , 2005 Oct. 1 : 885-91
  • Saiman L, Mayer-Hamblett N, Campbell P, Marshall BC, Macrolide Study Group
    Heterogeneity of treatment response to azithromycin in patients with cystic fibrosis.
    American journal of respiratory and critical care medicine , 2005 Oct. : 1008-12
  • Kulich M, Rosenfeld M, Campbell J, Kronmal R, Gibson RL, Goss CH, Ramsey B
    Disease-specific reference equations for lung function in patients with cystic fibrosis.
    American journal of respiratory and critical care medicine , 2005 Oct. : 885-91
  • Chen ML, Tablizo MA, Kun S, Keens TG
    Diaphragm pacers as a treatment for congenital central hypoventilation syndrome.
    Expert review of medical devices , 2005 Sept. : 577-85
  • Overview of published evidence on outcomes with early diagnosis from large US observational studies.
    The Journal of pediatrics , 2005 Sept. : S11-4
  • Debley JS, Carter ER, Gibson RL, Rosenfeld M, Redding GJ
    The prevalence of ibuprofen-sensitive asthma in children: a randomized controlled bronchoprovocation challenge study.
    The Journal of pediatrics , 2005 Aug. : 147(2)233-8
  • Debley JS, Carter ER, Gibson RL, Rosenfeld M, Redding GJ
    The prevalence of ibuprofen-sensitive asthma in children: a randomized controlled bronchoprovocation challenge study.
    The Journal of pediatrics , 2005 Aug. : 233-8
  • Chen ML, Witmans MB, Tablizo MA, Jubran RF, Turkel SB, Tavaré CJ, Keens TG
    Disordered respiratory control in children with partial cerebellar resections.
    Pediatric pulmonology , 2005 July : 88-91
  • Carter ER, Debley JS, Redding GJ
    Changes in asthma prevalence and impact on health and function in Seattle middle-school children: 1995 vs 2003.
    Annals of allergy, asthma & immunology : official publication of the American College of Allergy, Asthma, & Immunology , 2005 June : 94(6)634-9
  • Deterding R, Retsch-Bogart G, Milgram L, Gibson R, Daines C, Zeitlin PL, Milla C, Marshall B, Lavange L, Engels J, Mathews D, Gorden J, Schaberg A, Williams J, Ramsey B, Cystic Fibrosis Foundation Therapeutics Development Network
    Safety and tolerability of denufosol tetrasodium inhalation solution, a novel P2Y2 receptor agonist: results of a phase 1/phase 2 multicenter study in mild to moderate cystic fibrosis.
    Pediatric pulmonology , 2005 Apr, : 39(4)339-48
  • Deterding R, Retsch-Bogart G, Milgram L, Gibson R, Daines C, Zeitlin PL, Milla C, Marshall B, Lavange L, Engels J, Mathews D, Gorden J, Schaberg A, Williams J, Ramsey B
    Safety and tolerability of denufosol tetrasodium inhalation solution, a novel P2Y2 receptor agonist: results of a phase 1/phase 2 multicenter study in mild to moderate cystic fibrosis.
    Pediatric pulmonology , 2005 Apr, : 339-48
  • Moss RB, Mayer-Hamblett N, Wagener J, Daines C, Hale K, Ahrens R, Gibson RL, Anderson P, Retsch-Bogart G, Nasr SZ, Noth I, Waltz D, Zeitlin P, Ramsey B, Starko K
    Randomized, double-blind, placebo-controlled, dose-escalating study of aerosolized interferon gamma-1b in patients with mild to moderate cystic fibrosis lung disease.
    Pediatric pulmonology , 2005 Mar. : 209-18
  • Debley JS, Smith JM, Redding GJ, Critchlow CW
    Childhood asthma hospitalization risk after cesarean delivery in former term and premature infants.
    Annals of allergy, asthma & immunology : official publication of the American College of Allergy, Asthma, & Immunology , 2005 Feb. : 94(2)228-33
  • Mayer-Hamblett N, Kronmal RA
    Improving the estimation of change from baseline in a continuous outcome measure in the clinical trial setting.
    Contemporary clinical trials , 2005 Feb. : 2-16
  • Lynn Chen M, Davidson Ward SL, Keens T, Lin Z, K Khoo M
    Cardio-respiratory Uncoupling in Congenital Central Hypoventilation Syndrome.
    Conference proceedings : ... Annual International Conference of the IEEE Engineering in Medicine and Biology Society. IEEE Engineering in Medicine and Biology Society. Conference , 2005 : 4412-5
  • The Respiratory System
    Nelson Essential Pediatrics, 5th Edition , 2005 : 133-138
  • Beckmann C, Brittnacher M, Ernst R, Mayer-Hamblett N, Miller SI, Burns JL
    Use of phage display to identify potential Pseudomonas aeruginosa gene products relevant to early cystic fibrosis airway infections.
    Infection and immunity , 2005 Jan. : 444-52
  • An oral health curriculum for medical students at the University of Washington
    Acad Med , 2005 : 80434-442
  • Respiratory Mechanics
    Pediatric Pulmonary Function Testing , 2005 : 3320-33
  • Response to nonprescription epinephrine inhaler during nocturnal asthma.
    Ann Allergy Asthma Immunol , 2005 : 95530-4
  • Debley JS, Redding GJ, Critchlow CW
    Impact of adolescence and gender on asthma hospitalization: a population-based birth cohort study.
    Pediatric pulmonology , 2004 Dec. : 38(6)443-50
  • Sorensen MD, Galansky SH, Striegl AM, Koyle MA
    Prenatal bilateral extravaginal testicular torsion--a case presentation.
    Pediatric surgery international , 2004 Dec. : 20(11-12)892-3
  • Goss CH, Mayer-Hamblett N, Aitken ML, Rubenfeld GD, Ramsey BW
    Association between Stenotrophomonas maltophilia and lung function in cystic fibrosis.
    Thorax , 2004 Nov. : 955-9
  • Goss CH, Rosenfeld M
    Update on cystic fibrosis epidemiology.
    Current opinion in pulmonary medicine , 2004 Nov. : 510-4
  • Grosse SD, Boyle CA, Botkin JR, Comeau AM, Kharrazi M, Rosenfeld M, Wilfond BS
    Newborn screening for cystic fibrosis: evaluation of benefits and risks and recommendations for state newborn screening programs.
    MMWR. Recommendations and reports : Morbidity and mortality weekly report. Recommendations and reports / Centers for Disease Control , 2004 Oct. : 1-36
  • Chen ML, Keens TG
    Congenital central hypoventilation syndrome: not just another rare disorder.
    Paediatric respiratory reviews , 2004 Sept. : 182-9
  • Standaert TA, Boitano L, Emerson J, Milgram LJ, Konstan MW, Hunter J, Berclaz PY, Brass L, Zeitlin PL, Hammond K, Davies Z, Foy C, Noone PG, Knowles MR
    Standardized procedure for measurement of nasal potential difference: an outcome measure in multicenter cystic fibrosis clinical trials.
    Pediatric pulmonology , 2004 May : 385-92
  • Moskowitz SM, Foster JM, Emerson J, Burns JL
    Clinically feasible biofilm susceptibility assay for isolates of Pseudomonas aeruginosa from patients with cystic fibrosis.
    Journal of clinical microbiology , 2004 May : 1915-22
  • Combs C, Soares JJ, O'Connell JV, D'Angelo LJ, Pugatch D
    Sexual risk behaviors and polysubstance use in young intranasal heroin users.
    Substance abuse : official publication of the Association for Medical Education and Research in Substance Abuse , 2004 Mar. : 25(1)61-2
  • Moss RB, Rodman D, Spencer LT, Aitken ML, Zeitlin PL, Waltz D, Milla C, Brody AS, Clancy JP, Ramsey B, Hamblett N, Heald AE
    Repeated adeno-associated virus serotype 2 aerosol-mediated cystic fibrosis transmembrane regulator gene transfer to the lungs of patients with cystic fibrosis: a multicenter, double-blind, placebo-controlled trial.
    Chest , 2004 Feb. : 509-21
  • Ordoñez CL, Henig NR, Mayer-Hamblett N, Accurso FJ, Burns JL, Chmiel JF, Daines CL, Gibson RL, McNamara S, Retsch-Bogart GZ, Zeitlin PL, Aitken ML
    Inflammatory and microbiologic markers in induced sputum after intravenous antibiotics in cystic fibrosis.
    American journal of respiratory and critical care medicine , 2003 Dec. : 1471-5
  • Ernst RK, D'Argenio DA, Ichikawa JK, Bangera MG, Selgrade S, Burns JL, Hiatt P, McCoy K, Brittnacher M, Kas A, Spencer DH, Olson MV, Ramsey BW, Lory S, Miller SI
    Genome mosaicism is conserved but not unique in Pseudomonas aeruginosa isolates from the airways of young children with cystic fibrosis.
    Environmental microbiology , 2003 Dec. : 1341-9
  • Rosenfeld M, Ramsey BW, Gibson RL
    Pseudomonas acquisition in young patients with cystic fibrosis: pathophysiology, diagnosis, and management.
    Current opinion in pulmonary medicine , 2003 Nov. : 492-7
  • Rosenfeld M, Ramsey BW, Gibson RL
    Pseudomonas acquisition in young patients with cystic fibrosis: pathophysiology, diagnosis, and management.
    Current opinion in pulmonary medicine , 2003 Nov. : 492-7
  • Gibson RL, Burns JL, Ramsey BW
    Pathophysiology and management of pulmonary infections in cystic fibrosis.
    American journal of respiratory and critical care medicine , 2003 Oct. 15 : 918-51
  • Saiman L, Marshall BC, Mayer-Hamblett N, Burns JL, Quittner AL, Cibene DA, Coquillette S, Fieberg AY, Accurso FJ, Campbell PW 3rd, Macrolide Study Group
    Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: a randomized controlled trial.
    JAMA : the journal of the American Medical Association , 2003 Oct. : 1749-56
  • Qin X, Emerson J, Stapp J, Stapp L, Abe P, Burns JL
    Use of real-time PCR with multiple targets to identify Pseudomonas aeruginosa and other nonfermenting gram-negative bacilli from patients with cystic fibrosis.
    Journal of clinical microbiology , 2003 Sept. : 4312-7
  • Harding CO, Pillers DA, Steiner RD, Bottiglieri T, Rosenblatt DS, Debley J, Michael Gibson K
    Potential for misdiagnosis due to lack of metabolic derangement in combined methylmalonic aciduria/hyperhomocysteinemia (cblC) in the neonate.
    Journal of perinatology : official journal of the California Perinatal Association , 2003 July : 23(5)384-6
  • Sorensen MD, Galansky SH, Striegl AM, Mevorach R, Koyle MA
    Perinatal extravaginal torsion of the testis in the first month of life is a salvageable event.
    Urology , 2003 July : 62(1)132-4
  • Piedra PA, Cron SG, Jewell A, Hamblett N, McBride R, Palacio MA, Ginsberg R, Oermann CM, Hiatt PW, Purified Fusion Protein Vaccine Study Group
    Immunogenicity of a new purified fusion protein vaccine to respiratory syncytial virus: a multi-center trial in children with cystic fibrosis.
    Vaccine , 2003 June : 2448-60
  • Kulich M, Rosenfeld M, Goss CH, Wilmott R
    Improved survival among young patients with cystic fibrosis.
    The Journal of pediatrics , 2003 June : 631-6
  • Smith AL, Fiel SB, Mayer-Hamblett N, Ramsey B, Burns JL
    Susceptibility testing of Pseudomonas aeruginosa isolates and clinical response to parenteral antibiotic administration: lack of association in cystic fibrosis.
    Chest , 2003 May : 1495-502
  • Gibson RL, Emerson J, McNamara S, Burns JL, Rosenfeld M, Yunker A, Hamblett N, Accurso F, Dovey M, Hiatt P, Konstan MW, Moss R, Retsch-Bogart G, Wagener J, Waltz D, Wilmott R, Zeitlin PL, Ramsey B
    Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis.
    American journal of respiratory and critical care medicine , 2003 Mar. 15 : 841-9
  • Aitken ML, Greene KE, Tonelli MR, Burns JL, Emerson JC, Goss CH, Gibson RL
    Analysis of sequential aliquots of hypertonic saline solution-induced sputum from clinically stable patients with cystic fibrosis.
    Chest , 2003 Mar. : 792-9
  • Gibson RL, Emerson J, McNamara S, Burns JL, Rosenfeld M, Yunker A, Hamblett N, Accurso F, Dovey M, Hiatt P, Konstan MW, Moss R, Retsch-Bogart G, Wagener J, Waltz D, Wilmott R, Zeitlin PL, Ramsey B
    Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis.
    American journal of respiratory and critical care medicine , 2003 Mar. : 841-9
  • Gibson RL, Emerson J, McNamara S, Burns JL, Rosenfeld M, Yunker A, Hamblett N, Accurso F, Dovey M, Hiatt P, Konstan MW, Moss R, Retsch-Bogart G, Wagener J, Waltz D, Wilmott R, Zeitlin PL, Ramsey B
    Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis.
    American journal of respiratory and critical care medicine , 2003 Mar. : 841-9
  • Preparing graduates for the first year of residency: are medical schools meeting the need?
    Acad Med , 2003 : 7839-44
  • Geller DE, Rosenfeld M, Waltz DA, Wilmott RW
    Efficiency of pulmonary administration of tobramycin solution for inhalation in cystic fibrosis using an improved drug delivery system.
    Chest , 2003 Jan. : 28-36
  • Asthma
    Primary care of children, infants and adolescents , 2003 : J.A.Fox (ed)(St. Louis: Mosby)
  • Mayer-Hamblett N, Rosenfeld M, Emerson J, Goss CH, Aitken ML
    Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality.
    American journal of respiratory and critical care medicine , 2002 Dec. 15 : 1550-5
  • Goss CH, Mayer-Hamblett N, Kronmal RA, Ramsey BW
    The cystic fibrosis therapeutics development network (CF TDN): a paradigm of a clinical trials network for genetic and orphan diseases.
    Advanced drug delivery reviews , 2002 Dec. : 1505-28
  • Mayer-Hamblett N, Rosenfeld M, Emerson J, Goss CH, Aitken ML
    Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality.
    American journal of respiratory and critical care medicine , 2002 Dec. : 1550-5
  • Mayer-Hamblett N, Rosenfeld M, Emerson J, Goss CH, Aitken ML
    Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality.
    American journal of respiratory and critical care medicine , 2002 Dec. : 1550-5
  • To cohort or not to cohort: how transmissible is Pseudomonas aeruginosa?
    American journal of respiratory and critical care medicine , 2002 Oct. 1 : 906-7
  • Emerson J, Rosenfeld M, McNamara S, Ramsey B, Gibson RL
    Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis.
    Pediatric pulmonology , 2002 Aug. : 91-100
  • Emerson J, Rosenfeld M, McNamara S, Ramsey B, Gibson RL
    Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis.
    Pediatric pulmonology , 2002 Aug. : 91-100
  • Geller DE, Pitlick WH, Nardella PA, Tracewell WG, Ramsey BW
    Pharmacokinetics and bioavailability of aerosolized tobramycin in cystic fibrosis.
    Chest , 2002 July : 219-26
  • Cieri MV, Mayer-Hamblett N, Griffith A, Burns JL
    Correlation between an in vitro invasion assay and a murine model of Burkholderia cepacia lung infection.
    Infection and immunity , 2002 Mar. : 1081-6
  • Noone PG, Hamblett N, Accurso F, Aitken ML, Boyle M, Dovey M, Gibson R, Johnson C, Kellerman D, Konstan MW, Milgram L, Mundahl J, Retsch-Bogort G, Rodman D, Williams-Warren J, Wilmott RW, Zeitlin P, Ramsey B, Cystic Fibrosis Therapeutics Development Research Group
    Safety of aerosolized INS 365 in patients with mild to moderate cystic fibrosis: results of a phase I multi-center study.
    Pediatric pulmonology , 2001 Aug. : 122-8
  • Mayer-Hamblett N, Self S
    A regression modeling approach for describing patterns of HIV genetic variation.
    Biometrics , 2001 June : 449-60
  • A Follow-up Study of the Characteristics of Dean's Letter
    Acad Med , 2001 : 76727-73
  • From concept to culture: The WWAMI program at the University of Washington School of Medicine
    Acad Med , 2001 : 76765-775
  • Inspiratory Resistive Load Detection in Children with Life-threatening Asthma
    Pediatr Pulmonol , 2001 : 3244-48
  • Respiratory System
    Cystic Fibrosis , 2000
  • A National General Pediatric Clerkship Curriculum: The Process of Development and Implementation
    Pediatrics , 2000 : 106216-222
  • Respiratory Mechanics. In Pediatric Pulmonary Function Testing
    Respiratory System: Pediatrics. In Cystic Fibrosis , 2000 : . 204-218
  • Respiratory related evoked potential in children with life-threatening asthma
    Am J Respir Crit Care Med , 2000 : 161(6)1830-5
  • What parents of children with asthma tell us.
    Journal of Pediatric Health Care , 2000 : 3122-6
  • The asthma outreach project: A promising approach to comprehensive asthma management
    Journal of Asthma , 1998 : 1119-27
  • Attachment and Entry of Influenza Virus into Host Cells: Pivotal Roles of the Hemagglutinin
    Structural Biology of Viruses , 1997
  • Magnitude estimation of inspiratory resistive loads in children with life-threatening asthma.
    Am J Respir Crit Care Med , 1997 : 156(5)1530-5
  • The Low pH-induced Conformational Change in the Influenza Hemagglutinin: Inhibitor Design
    PhD thesis, UCSF , 1996
  • Fusion Mechanism of the Influenza Hemagglutinin: Inhibitor Design
    Options for the Control of Influenza III: Proceedings , 1996
  • Perinatal buprenorphine exposure affects behavioral and cholinergic development in the rat [abstract
    Problems of drug dependence 1995: Proceedings of the 57th annual scientific meeting , 1996 : 168348
  • Regulation of the manganese superoxide dismutase and inducible nitric oxide synthase gene in rat neuronal and glial cells
    J Neurochem , 1996 : 662128-35
  • Abstracts available upon request.
  • Abstracts - Available upon request
  • Revision surgeries are associated with significant increased risk of subsequent cerebrospinal fluid shunt infection
    Pediatric Disease Journal (In press)
  • How aspirin works
    http://health.howstuffworks.com/aspirin.htm
  • Abstracts available upon request
  • Abstracts - Available upon request